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[Ciliary changes with abscence of dynein arms in Kartagener's syndrome]. / Alteración ciliar con ausencia de los brazos de dineina en el síndrome de Kartagener.
Melgarejo Moreno, P; Galindo Ortego, X; Marqués Amat, L; Torres Cortada, G; Hellin Meseger, D; García González, B.
Afiliación
  • Melgarejo Moreno P; Unitat d'Al-lergologia, Hospital de Santa María de Lleida.
Acta Otorrinolaringol Esp ; 55(3): 145-7, 2004 Mar.
Article en Es | MEDLINE | ID: mdl-15253342
ABSTRACT
A 33 years-old female with a diagnosis of Kartagener's syndrome was studied. She had a clinical history of chronic sinusitis with nasal obstruction and rhinorrea, and a chronic cough with mucopurulent sputum. A paranasal sinus CT showed hypertrophyc mucosa. A thoracic CT showed a situs inversus and chronic bronchitis with bronchiectasis. The saccharin test lasted 55 minutes. The electron microscopy study showed in a a cross-sectional axoneme a total absence of the outer and inner arm of the 9th outer doublet in over a 100 cilias studied. No others ultrastructure anormalities were observed.
Asunto(s)
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Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Síndrome de Kartagener / Dineínas Límite: Adult / Female / Humans Idioma: Es Revista: Acta Otorrinolaringol Esp Año: 2004 Tipo del documento: Article
Buscar en Google
Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Síndrome de Kartagener / Dineínas Límite: Adult / Female / Humans Idioma: Es Revista: Acta Otorrinolaringol Esp Año: 2004 Tipo del documento: Article