Otolaryngologic manifestations of PHACE syndrome.
Int J Pediatr Otorhinolaryngol
; 68(11): 1445-50, 2004 Nov.
Article
en En
| MEDLINE
| ID: mdl-15488979
ABSTRACT
Two case reports of PHACE syndrome (posterior fossa malformations (P), hemangiomas (H), arterial anomalies (A), coarctation of the aorta and cardiac defects (C), and eye abnormalities (E)) are presented. Clinical characteristics consisted of cutaneous and airway hemangiomas, aortic coarctation, and left superior vena cava in one child and cutaneous and airway hemangiomas, sternal clefting, and supraumbilical raphe in the other child. Treatment modalities included systemic and intralesional steroids for cutaneous and airway hemangiomas, submucosal resection and laryngotracheal reconstruction for airway hemangiomas, repair of aortic coarctation, and laser treatment of cutaneous hemangiomas. PHACE syndrome poses a significant potential for airway compromise from hemangiomas, which may require multimodality treatment.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Neoplasias Laríngeas
/
Síndromes Neurocutáneos
/
Hemangioma
Tipo de estudio:
Etiology_studies
Límite:
Female
/
Humans
/
Infant
/
Newborn
Idioma:
En
Revista:
Int J Pediatr Otorhinolaryngol
Año:
2004
Tipo del documento:
Article
País de afiliación:
Estados Unidos