Pulmonary lymphangioleiomyomatosis followed by a localized retroperitoneal lymphangioleiomyoma.
APMIS
; 114(11): 821-4, 2006 Nov.
Article
en En
| MEDLINE
| ID: mdl-17078865
ABSTRACT
Lymphangioleiomyomatosis is a rare disease that affects females of reproductive age. Microscopically, it is characterized by abnormal proliferation of immature smooth muscle-like cells that grow diffusely in the lung. Extrapulmonary manifestations in the mediastinum, peritoneum and pelvic lymph nodes are uncommon. We here describe a patient who initially presented with pulmonary lymphangioleiomyomatosis and subsequently developed a localized retroperitoneal mass. Pathologic examination showed that the mass was a lymphangioleiomyoma. The result of the immunohistochemical study was the same as that for the pulmonary lesion. It is therefore suggested that metastatic lymphangioleiomyoma should be included in the differential diagnosis in the patient with pulmonary lymphangioleiomyomatosis presenting with an extrapulmonary lesion.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Neoplasias Retroperitoneales
/
Linfangioleiomiomatosis
/
Neoplasias Pulmonares
/
Linfangiomioma
Tipo de estudio:
Diagnostic_studies
Límite:
Adult
/
Female
/
Humans
Idioma:
En
Revista:
APMIS
Asunto de la revista:
ALERGIA E IMUNOLOGIA
/
MICROBIOLOGIA
/
PATOLOGIA
Año:
2006
Tipo del documento:
Article
País de afiliación:
Taiwán