Pseudomyxoma peritonei--case report.

ABSTRACT

The syndrome pseudomyxoma peritonei is rare, present in only 2/10,000 laparotomies. We report the case of a 58-year-old woman with a primary tumor of the appendix, and secondary involvement of other structures and organs of the abdominal cavity. In our case, we performed maximal surgical reduction of the tumor, with remaining implants on diaphragmatic domes and liver, as we did not have technical conditions to safely perform prolonged surgery which would have included a surgical procedure on the liver and administration of intraoperative chemotherapy. The patient underwent six series of parenteral chemotherapy, but refused the second-look surgery. Even though our patient did not receive intraperitoneal chemotherapy, maximal surgical tumor reduction, and refused second-look surgery, she is still alive and without any major complaints two years after the surgery.