A case series of congenital hepatic hilar cyst: recommendations for diagnosis and management.
Isr Med Assoc J
; 17(1): 32-6, 2015 Jan.
Article
en En
| MEDLINE
| ID: mdl-25739174
ABSTRACT
BACKGROUND:
Congenital hepatic hilar cysts are rare. Some are simple and do not require intervention, but some biliary cystic malformations impose the risk of morbidity and mortality.OBJECTIVES:
To assess a series of five patients presenting with congenital hepatic hilar cysts.METHODS:
We retrospectively reviewed all cases presenting to our pediatric surgical service between January 2010 and December 2012 and found to have a congenital hepatic hilar cyst. Data regarding clinical, radiological, operative and pathological features were analyzed.RESULTS:
Five children with congenital cyst of the hepatic hilum were identified; four of them were diagnosed prenatally. Four children had undergone surgical intervention one with intrahepatic choledochal cyst, one with epidermoid cyst, and two with biliary atresia and an associated cyst of the common bile duct. In another case of choledochal cyst the treatment was conservative. All children except one had a good prognosis; one child with biliary atresia required liver transplantation.CONCLUSIONS:
The differential diagnosis of congenital hepatic hilar cyst includes a broad spectrum of pathologies. It is essential to diagnose biliary atresia as early as possible. Signs such as smaller cysts in association with a hypoplastic gallbladder and direct hyperbilirubinemia may be suggestive of biliary atresia.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Atresia Biliar
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Quiste del Colédoco
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Quistes
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Hepatopatías
Tipo de estudio:
Diagnostic_studies
/
Guideline
/
Observational_studies
/
Prognostic_studies
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Risk_factors_studies
Límite:
Female
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Humans
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Infant
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Male
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Newborn
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Pregnancy
Idioma:
En
Revista:
Isr Med Assoc J
Asunto de la revista:
MEDICINA
Año:
2015
Tipo del documento:
Article