Hearing loss associated with progressive ataxia (Lichtenstein-Knorr disease?). Report of a sporadic case with peculiar neuroradiological findings.
Acta Neurol (Napoli)
; 11(5): 351-9, 1989 Oct.
Article
en En
| MEDLINE
| ID: mdl-2603781
ABSTRACT
A sporadic case of hearing loss with ataxia, clinically suggesting Lichtenstein-Knorr disease, is described. Magnetic Resonance (MR) shows an involvement of the white matter, which appears diffusely reduced and abnormal, together with a peculiar tickening of the grey matter. The possible relationships with leukodystrophies and with generalized cortical dysplasias are discussed. To our knowledge, MR imaging has never been performed in Lichtenstein-Knorr disease.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Imagen por Resonancia Magnética
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Ataxia Cerebelosa
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Pérdida Auditiva Bilateral
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Pérdida Auditiva
Tipo de estudio:
Diagnostic_studies
/
Risk_factors_studies
Límite:
Child
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Female
/
Humans
Idioma:
En
Revista:
Acta Neurol (Napoli)
Año:
1989
Tipo del documento:
Article