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Differential Toxicity of Nuclear RNA Foci versus Dipeptide Repeat Proteins in a Drosophila Model of C9ORF72 FTD/ALS.
Tran, Helene; Almeida, Sandra; Moore, Jill; Gendron, Tania F; Chalasani, UmaDevi; Lu, Yubing; Du, Xing; Nickerson, Jeffrey A; Petrucelli, Leonard; Weng, Zhiping; Gao, Fen-Biao.
Afiliación
  • Tran H; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Almeida S; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Moore J; Program in Bioinformatics and Integrative Biology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Gendron TF; Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
  • Chalasani U; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Lu Y; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Du X; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Nickerson JA; Department of Cell and Developmental Biology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Petrucelli L; Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
  • Weng Z; Program in Bioinformatics and Integrative Biology, University of Massachusetts Medical School, Worcester, MA 01605, USA.
  • Gao FB; Department of Neurology, University of Massachusetts Medical School, Worcester, MA 01605, USA. Electronic address: fen-biao.gao@umassmed.edu.
Neuron ; 87(6): 1207-1214, 2015 Sep 23.
Article en En | MEDLINE | ID: mdl-26402604

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: ARN Nuclear / Proteínas / Dipéptidos / Modelos Animales de Enfermedad / Demencia Frontotemporal / Esclerosis Amiotrófica Lateral Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Neuron Asunto de la revista: NEUROLOGIA Año: 2015 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: ARN Nuclear / Proteínas / Dipéptidos / Modelos Animales de Enfermedad / Demencia Frontotemporal / Esclerosis Amiotrófica Lateral Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Neuron Asunto de la revista: NEUROLOGIA Año: 2015 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos