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Pivotal role of inter-organ aspartate metabolism for treatment of mitochondrial aspartate-glutamate carrier 2 (citrin) deficiency, based on the mouse model.
Saheki, Takeyori; Moriyama, Mitsuaki; Kuroda, Eishi; Funahashi, Aki; Yasuda, Izumi; Setogawa, Yoshiko; Gao, Qinghua; Ushikai, Miharu; Furuie, Sumie; Yamamura, Ken-Ichi; Takano, Katsura; Nakamura, Yoichi; Eto, Kazuhiro; Kadowaki, Takashi; Sinasac, David S; Furukawa, Tatsuhiko; Horiuchi, Masahisa; Tai, Yen How.
Afiliación
  • Saheki T; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan. takesah@gmail.com.
  • Moriyama M; Laboratory for Yamamura Projects, Institute for Resource Development and Analysis, Kumamoto, Kumamoto, Japan. takesah@gmail.com.
  • Kuroda E; Laboratory of Integrative Physiology in Veterinary Sciences, Osaka Prefecture University, Izumisano, Osaka, Japan.
  • Funahashi A; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Yasuda I; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Setogawa Y; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Gao Q; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Ushikai M; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Furuie S; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Yamamura KI; Laboratory for Yamamura Projects, Institute for Resource Development and Analysis, Kumamoto, Kumamoto, Japan.
  • Takano K; Laboratory for Yamamura Projects, Institute for Resource Development and Analysis, Kumamoto, Kumamoto, Japan.
  • Nakamura Y; Laboratory of Integrative Physiology in Veterinary Sciences, Osaka Prefecture University, Izumisano, Osaka, Japan.
  • Eto K; Laboratory of Integrative Physiology in Veterinary Sciences, Osaka Prefecture University, Izumisano, Osaka, Japan.
  • Kadowaki T; Department of Internal Medicine, Teikyo University, Tokyo, Japan.
  • Sinasac DS; Department of Diabetes and Metabolic Diseases, Graduate School of Medicine, The University of Tokyo, Tokyo, Japan.
  • Furukawa T; Alberta Children's Hospital Research Institute, Department of Medical Genetics, Cumming School of Medicine, University of Calgary, Calgary, Alberta, Canada.
  • Horiuchi M; Department of Molecular Oncology, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
  • Tai YH; Department of Hygiene and Health Promotion Medicine, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Kagoshima, Japan.
Sci Rep ; 9(1): 4179, 2019 03 12.
Article en En | MEDLINE | ID: mdl-30862943

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Especificidad de Órganos / Ácido Aspártico / Citrulinemia / Proteínas de Transporte de Membrana Mitocondrial Límite: Animals Idioma: En Revista: Sci Rep Año: 2019 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Especificidad de Órganos / Ácido Aspártico / Citrulinemia / Proteínas de Transporte de Membrana Mitocondrial Límite: Animals Idioma: En Revista: Sci Rep Año: 2019 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Reino Unido