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Intrathecal rituximab in immunoglobulin G4-hypertrophic pachymeningitis.
Soares, Carolina; Martins, Diana F; Pestana-Silva, Roberto; Honavar, Mrinalini; Faria, Olinda; Abreu, Pedro; Costa, Andreia.
Afiliación
  • Soares C; Department of Neurology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal; Department of Clinic Neurosciences and Mental Health, Faculty of Medicine of University of Porto, Porto, Portugal. Electronic address: carolina.soares@chsj.min-saude.pt.
  • Martins DF; Department of Anatomic Pathology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal.
  • Pestana-Silva R; Department of Anatomic Pathology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal.
  • Honavar M; Department of Anatomic Pathology, ULS de Matosinhos - Hospital de Pedro Hispano, Matosinhos, Portugal.
  • Faria O; Department of Ophthalmology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal.
  • Abreu P; Department of Neurology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal; Department of Clinic Neurosciences and Mental Health, Faculty of Medicine of University of Porto, Porto, Portugal.
  • Costa A; Department of Neurology, Centro Hospitalar Universitário de São João, E.P.E., Porto, Portugal; Department of Clinic Neurosciences and Mental Health, Faculty of Medicine of University of Porto, Porto, Portugal.
J Neuroimmunol ; 334: 576997, 2019 09 15.
Article en En | MEDLINE | ID: mdl-31254930
ABSTRACT
We describe the case of a 69-year-old man who presented with symptoms of headache and severe vision loss due to G4 immunoglobulin (IgG4) hypertrophic pachymeningitis (HP). The patient was initially responsive to corticotherapy, but vision loss progressed when steroid therapy was first tapered. No improvement was noticed with intravenous rituximab. The patient showed clinical and radiological improvement after intrathecal rituximab, which can be an efficacious alternative treatment option.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Inmunoglobulina G / Rituximab / Antineoplásicos Inmunológicos / Meningitis Límite: Aged / Humans / Male Idioma: En Revista: J Neuroimmunol Año: 2019 Tipo del documento: Article

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Inmunoglobulina G / Rituximab / Antineoplásicos Inmunológicos / Meningitis Límite: Aged / Humans / Male Idioma: En Revista: J Neuroimmunol Año: 2019 Tipo del documento: Article