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A rare vascular lesion of newborn: cutis marmorata telangiectatica congenital.
Ergon, Ezgi Yangin; Çelik, Kiymet; Çolak, Rüya; Özdemir, Senem Alkan; Olukman, Özgür; Kundak, Selcen; Çalkavur, Sebnem.
Afiliación
  • Ergon EY; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Çelik K; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Çolak R; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Özdemir SA; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Olukman Ö; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Kundak S; Department of Dermatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
  • Çalkavur S; Department of Neonatology, Izmir Dr. Behçet Uz Children's Hospital, Izmir, Turkey.
Turk Pediatri Ars ; 54(2): 133-136, 2019.
Article en En | MEDLINE | ID: mdl-31384150
ABSTRACT
Cutis marmorata telangiectatica congenita is a rare, benign, sporadic and cutaneous vascular disease. A newborn female baby whose mother was aged 29 years and used propylthiouracil during pregnancy was hospitalized because of varicose lesions on the skin of the lower extremity and on the back, which were present at birth. It was observed that the lesions did not disappear, although appropriate room temperature was provided. The patient was diagnosed as having cutis marmorata telangiectatica congenita and screened for additional anomalies. She had no additional anomalies, and she was discharged and monitored. At the postnatal sixth month, the cutaneous vascular lesions disappeared spontaneously. Cutis marmorata telangiectatica congenita, which is a rare condition, should be kept in mind in the differential diagnosis of physiologic cutis marmoratus, which occurs frequently in the neonatal period.
RESUMEN
Kutis marmorata telenjiektatika konjenita; nadir görülen, selim, sporadik, deriyi tutan vasküler bir hastaliktir. Yirmi dokuz yasinda hipertroidi nedeni ile propiltiyourasil kullanan anneden dogan kiz bebek, her iki alt ekstremitede ve sirtta yerlesim gösteren renk degisikliginin eslik ettigi variköz lezyonlar nedeniyle yatirildi, lezyonlarin uygun ortam sicakligi saglanmasina ragmen düzelmedigi saptandi. Kutis marmorata telenjiektatika konjenita tanisi konan olgu; eslik edebilecek ek anomaliler açisindan tarandi; ek anomali saptanmayan olgu taburcu edilerek izleme alindi, postnatal altinci ayda kutanöz vasküler lezyonlarin kendiliginden kayboldugu görüldü. Yenidogan döneminde sik olarak karsimiza çikan fizyolojik kutis marmoratus ayirici tanisinda, ender görülen bir durum olan kutis marmorata telenjiektatika konjenita da akilda tutulmalidir.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Turk Pediatri Ars Año: 2019 Tipo del documento: Article País de afiliación: Turquía

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Turk Pediatri Ars Año: 2019 Tipo del documento: Article País de afiliación: Turquía