Primary tracheocutaneous fistula closure with immediate transition to nocturnal noninvasive positive pressure ventilation in two children with Congenital Central Hypoventilation Syndrome.
Int J Pediatr Otorhinolaryngol
; 134: 110019, 2020 Jul.
Article
en En
| MEDLINE
| ID: mdl-32247940
ABSTRACT
Transitioning children with Congenital Central Hypoventilation Syndrome (CCHS) from nocturnal invasive ventilation via tracheostomy to noninvasive positive pressure ventilation (NIPPV) is challenging due to the leak caused by the tracheocutaneous fistula (TCF), resulting in insufficient ventilation. Decannulation and primary closure of the TCF with immediate transition to nocturnal NIPPV was performed in two children with CCHS at a tertiary care children's hospital. Neither child developed significant adverse effects such as pneumomediastinum or pneumothorax. This technique is a novel approach that may improve decannulation outcomes and aid transition to NIPPV in this patient population.
Palabras clave
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Enfermedades de la Tráquea
/
Fístula del Sistema Respiratorio
/
Respiración con Presión Positiva
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Fístula Cutánea
/
Apnea Central del Sueño
/
Ventilación no Invasiva
/
Hipoventilación
Límite:
Child
/
Female
/
Humans
/
Male
Idioma:
En
Revista:
Int J Pediatr Otorhinolaryngol
Año:
2020
Tipo del documento:
Article
País de afiliación:
Estados Unidos