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Systemic deletion of Atp7b modifies the hepatocytes' response to copper overload in the mouse models of Wilson disease.
Muchenditsi, Abigael; Talbot, C Conover; Gottlieb, Aline; Yang, Haojun; Kang, Byunghak; Boronina, Tatiana; Cole, Robert; Wang, Li; Dev, Som; Hamilton, James P; Lutsenko, Svetlana.
Afiliación
  • Muchenditsi A; Department of Physiology, Johns Hopkins Medical Institutes, 725 N Wolfe street, Baltimore, MD, 21205, USA.
  • Talbot CC; Core Analysis Unit, Johns Hopkins Medical Institutes, Baltimore, MD, 21205, USA.
  • Gottlieb A; Department of Physiology, Johns Hopkins Medical Institutes, 725 N Wolfe street, Baltimore, MD, 21205, USA.
  • Yang H; Department of Physiology, Johns Hopkins Medical Institutes, 725 N Wolfe street, Baltimore, MD, 21205, USA.
  • Kang B; Department of Molecular and Comparative Pathobiology, Johns Hopkins Medical Institutes, Baltimore, MD, 21205, USA.
  • Boronina T; Novartis Institutes for Biomedical Research, Cambridge, MA, USA.
  • Cole R; Mass Spectrometry and Proteomics Facility, Johns Hopkins Medical Institutes, Baltimore, MD, 21205, USA.
  • Wang L; Mass Spectrometry and Proteomics Facility, Johns Hopkins Medical Institutes, Baltimore, MD, 21205, USA.
  • Dev S; Department of Physiology, Johns Hopkins Medical Institutes, 725 N Wolfe street, Baltimore, MD, 21205, USA.
  • Hamilton JP; Department of Physiology, Johns Hopkins Medical Institutes, 725 N Wolfe street, Baltimore, MD, 21205, USA.
  • Lutsenko S; Department of Medicine, Johns Hopkins Medical Institutes, Baltimore, MD, 21205, USA.
Sci Rep ; 11(1): 5659, 2021 03 11.
Article en En | MEDLINE | ID: mdl-33707579

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Eliminación de Gen / Cobre / Hepatocitos / ATPasas Transportadoras de Cobre / Degeneración Hepatolenticular Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Sci Rep Año: 2021 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Eliminación de Gen / Cobre / Hepatocitos / ATPasas Transportadoras de Cobre / Degeneración Hepatolenticular Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Sci Rep Año: 2021 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Reino Unido