Your browser doesn't support javascript.
loading
Loss of mitochondrial fatty acid ß-oxidation protein short-chain Enoyl-CoA hydratase disrupts oxidative phosphorylation protein complex stability and function.
Burgin, Harrison; Sharpe, Alice J; Nie, Shuai; Ziemann, Mark; Crameri, Jordan J; Stojanovski, Diana; Pitt, James; Ohtake, Akira; Murayama, Kei; McKenzie, Matthew.
Afiliación
  • Burgin H; School of Life and Environmental Sciences, Faculty of Science, Engineering and Built Environment, Deakin University, Geelong, Australia.
  • Sharpe AJ; Department of Biochemistry and Molecular Biology, Monash Biomedicine Discovery Institute, Monash University, Melbourne, Australia.
  • Nie S; Melbourne Mass Spectrometry and Proteomics Facility, Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Australia.
  • Ziemann M; School of Life and Environmental Sciences, Faculty of Science, Engineering and Built Environment, Deakin University, Geelong, Australia.
  • Crameri JJ; Department of Biochemistry and Pharmacology, Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Australia.
  • Stojanovski D; Department of Biochemistry and Pharmacology, Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Australia.
  • Pitt J; Department of Paediatrics, Victorian Clinical Genetics Services, Murdoch Childrens Research Institute, The University of Melbourne, Australia.
  • Ohtake A; Department of Pediatrics & Clinical Genomics, Faculty of Medicine, Saitama Medical University, Japan.
  • Murayama K; Centre for Intractable Diseases, Saitama Medical University Hospital, Japan.
  • McKenzie M; Department of Metabolism, Chiba Children's Hospital, Japan.
FEBS J ; 290(1): 225-246, 2023 01.
Article en En | MEDLINE | ID: mdl-35962613

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Fosforilación Oxidativa / Proteínas Mitocondriales Tipo de estudio: Prognostic_studies Límite: Humans Idioma: En Revista: FEBS J Asunto de la revista: BIOQUIMICA Año: 2023 Tipo del documento: Article País de afiliación: Australia Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Fosforilación Oxidativa / Proteínas Mitocondriales Tipo de estudio: Prognostic_studies Límite: Humans Idioma: En Revista: FEBS J Asunto de la revista: BIOQUIMICA Año: 2023 Tipo del documento: Article País de afiliación: Australia Pais de publicación: Reino Unido