[Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report]. / Mazabraud 증후군에서 발생한 ê³¨ìœ¡ì¢ ìœ¼ë¡œ ì• ì„± 변환: 증례 ë³´ê³ .

ABSTRACT

Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.