Management of Neurofibromatosis Type 2-Associated Vestibular Schwannomas.
Otolaryngol Clin North Am
; 56(3): 533-541, 2023 Jun.
Article
en En
| MEDLINE
| ID: mdl-36964092
ABSTRACT
Neurofibromatosis type 2 (NF2) is an autosomal dominant syndrome caused by a mutation in the NF2 suppressor gene and is characterized by the development of multiple benign tumors throughout the central nervous system. Bilateral vestibular schwannomas (VSs) are pathognomonic for NF2 and are associated with progressive hearing loss and eventual deafness in most patients. This review presents current management options for NF-2-associated VSs.
Palabras clave
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Neuroma Acústico
/
Neurofibromatosis 2
/
Pérdida Auditiva
Tipo de estudio:
Risk_factors_studies
Límite:
Humans
Idioma:
En
Revista:
Otolaryngol Clin North Am
Año:
2023
Tipo del documento:
Article
País de afiliación:
Estados Unidos