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A rare case of congenital lobar emphysema presenting as recurrent pneumonia in early adulthood: A case report and literature review.
Alrahil, Ali; Aljanadi, Mazen; Alslaiman, Rand; Mahjaa, Mohammad Tahsen; Alfandi, Abdullah; Absa, Ahmad Abo.
Afiliación
  • Alrahil A; Department of Thoracic Surgery, Damascus Hospital, Damascus, Syria. Electronic address: Alialrahil1994@gmail.com.
  • Aljanadi M; Department of Thoracic Surgery, Damascus Hospital, Damascus, Syria.
  • Alslaiman R; Pulmonology Department, Damascus Hospital, Damascus, Syria.
  • Mahjaa MT; Faculty of Medicine, Al-Sham Private University, Damascus, Syria.
  • Alfandi A; Faculty of Medicine, Al-Sham Private University, Damascus, Syria.
  • Absa AA; Thoracic Surgery Department, Damascus Hospital, Damascus, Syria.
Int J Surg Case Rep ; 120: 109852, 2024 Jul.
Article en En | MEDLINE | ID: mdl-38861815
ABSTRACT
INTRODUCTION AND

SIGNIFICANCE:

Congenital lobar emphysema (CLE) is a rare but important lung malformation typically discovered in the newborn period. Some rare cases are reported in adults. It can present with various respiratory symptoms. Diagnosis relies primarily on chest CT scans, and the main treatment is surgery. CASE PRESENTATION We present a case of a young girl with recurrent respiratory infections who was misdiagnosed with a pneumothorax. A chest tube was inserted. Later, CLE was identified, and the affected lung lobe was surgically removed. CLINICAL

DISCUSSION:

This case highlights the importance of including CLE in the differential diagnosis for hyperinflation of a lung lobe. A CT scan is crucial for confirmation.

CONCLUSION:

Congenital lobar emphysema is a rare disease that primarily affects children. Most children with CLE experience symptoms and require surgery. In adults, CLE is uncommon, and surgery is based on the severity of symptoms and radiological findings.
Palabras clave

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Int J Surg Case Rep Año: 2024 Tipo del documento: Article Pais de publicación: Países Bajos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Int J Surg Case Rep Año: 2024 Tipo del documento: Article Pais de publicación: Países Bajos