Bilateral cochlear fibrosis complicating chronic myeloid leukemia: A CARE case report.
Eur Ann Otorhinolaryngol Head Neck Dis
; 2024 Aug 07.
Article
en En
| MEDLINE
| ID: mdl-39117480
ABSTRACT
PURPOSE:
We report the second case of bilateral sudden sensorineural hearing loss with intracochlear fibrosis due to chronic myeloid leukemia. CASE REPORT A 44-year-old man presented to the emergency department with rapidly progressive bilateral hearing loss, tinnitus and vertigo, associated with dyspnea. Chronic myeloid leukemia complicated by pulmonary and cochleovestibular leukostasis was diagnosed, and cytoreductive treatment was started. Despite this treatment, bilateral total hearing loss and complete vestibular deficit persisted. MRI showed bilateral labyrinthitis, and emergency cochlear implantation was indicated. During surgery, inflammatory intracochlear tissue made electrode array insertion possible only against resistance. One year after implantation, there was significant improvement in speech recognition and communication scores.CONCLUSION:
In case of sudden sensorineural hearing loss induced by chronic myeloid leukemia, treatment should be as fast as possible, with prompt cochlear implantation in case of definitive profound hearing loss, because of the risk of cochlear fibrosis and ossification.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Idioma:
En
Revista:
Eur Ann Otorhinolaryngol Head Neck Dis
Año:
2024
Tipo del documento:
Article
Pais de publicación:
Francia