Living Donor Liver Transplantation for an Infant with Osteogenesis Imperfecta and Intrahepatic Cholestasis: Report of a Case
Journal of Korean Medical Science
; : 441-444, 2014.
Article
en En
| WPRIM
| ID: wpr-111999
Biblioteca responsable:
WPRO
ABSTRACT
Osteogenesis imperfecta (OI) is a group of genetic disorders characterized by bone fragility and connective tissue manifestations. We report a successful liver transplantation (LT) in an 8-month-old boy with OI and cholestatic biliary cirrhosis. After 4 cycles of intravenous pamidronate, LT was performed under intravenous anesthesia using a left lateral section from his mother without mechanical retractors. The operation time was 420 min and estimated blood loss was 520 mL requiring one unit of RBC transfusion. He was discharged without surgical complications. Therefore, LT should be considered for patients with end stage liver disease and OI under organic multidisciplinary cooperation.
Palabras clave
Texto completo:
1
Base de datos:
WPRIM
Asunto principal:
Osteogénesis Imperfecta
/
Densidad Ósea
/
Colestasis Intrahepática
/
Trasplante de Hígado
/
Donadores Vivos
/
Difosfonatos
/
Fracturas Óseas
/
Conservadores de la Densidad Ósea
Límite:
Humans
/
Infant
/
Male
Idioma:
En
Revista:
Journal of Korean Medical Science
Año:
2014
Tipo del documento:
Article