Joint Health Status in Hemophilia Patients Using Hemophilia Joint Health Score and Pettersson Score / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
; : 108-115, 2018.
Article
en Ko
| WPRIM
| ID: wpr-717646
Biblioteca responsable:
WPRO
ABSTRACT
BACKGROUND:
Comprehensive clinical and radiologic follow-up is needed to preserve joint functions and quality of life in hemophilia using clinimetric tools such as Hemophilia joint health score (HJHS) or Pettersson score (PS). We investigated the joint health status evaluated using the tools in Korean hemophilia patients.METHODS:
We reviewed retrospectively medical records to collect clinical parameters, HJHS and PS, who were followed up in Severance Hospital, Seoul, Korea. The correlation between HJHS and PS, and the effect of the prophylaxis for hemophilia on the outcomes measured with the scores were evaluated. The prophylaxis proportion (PP) was calculated as the proportion of prophylaxis duration to each patient's life time.RESULTS:
Total of 28 patients with severe hemophilia were enrolled. Twelve patients (42.8%) were less than 20 years old. Total of 23 patients had experienced prophylaxis during their lives, and median PP was 39.7%. There was significant correlation between HJHS and PS (P 20 years old.CONCLUSION:
HJHS and PS were positively correlated. Each score increased as the patient's age increased. The prophylaxis had protective effect on joint health. The prospective evaluation of HJHS and PS will be needed to prove the effect of proper management on the joint health status.Palabras clave
Texto completo:
1
Base de datos:
WPRIM
Asunto principal:
Calidad de Vida
/
Registros Médicos
/
Estado de Salud
/
Estudios Prospectivos
/
Estudios Retrospectivos
/
Estudios de Seguimiento
/
Evaluación del Resultado de la Atención al Paciente
/
Seúl
/
Hemofilia A
/
Articulaciones
Tipo de estudio:
Observational_studies
/
Prognostic_studies
Aspecto:
Determinantes_sociais_saude
/
Patient_preference
Límite:
Humans
País/Región como asunto:
Asia
Idioma:
Ko
Revista:
Clinical Pediatric Hematology-Oncology
Año:
2018
Tipo del documento:
Article