A Case of Serum Amino Acid Disturbance with Hyperammonemia in Patient with Primary Amyloidosis
Korean Journal of Hematology
; : 54-57, 2005.
Article
en Ko
| WPRIM
| ID: wpr-720447
Biblioteca responsable:
WPRO
ABSTRACT
There have been reports that hyperammonemia and amino acid disturbance can cause loss of consciousness in patients with multiple myelomas and normal liver function. We experienced a case of a 71-years-old female patient with amyloidosis, who had shown disturbance of consciousness. At that time, the serum ammonia level was elevated; serum amino acids disturbance was also noted. In particular, the decrease in branched-chain amino acids and increase in aromatic amino acids results in a low Fisher ratio. The Fisher ratio, the ratio of branched-chain to aromatic amino acids, has been suggested as an important indicator of consciousness disturbance. We report, for the first time in Korea, a case of amyloidosis, with mental disturbance due to serum amino acid disturbance.
Palabras clave
Texto completo:
1
Base de datos:
WPRIM
Asunto principal:
Inconsciencia
/
Estado de Conciencia
/
Hiperamonemia
/
Aminoácidos Aromáticos
/
Aminoácidos
/
Aminoácidos de Cadena Ramificada
/
Amoníaco
/
Amiloidosis
/
Corea (Geográfico)
/
Hígado
Límite:
Female
/
Humans
País/Región como asunto:
Asia
Idioma:
Ko
Revista:
Korean Journal of Hematology
Año:
2005
Tipo del documento:
Article