Pulmonary alveolar capillary dysplasia in infants: A rare and deadly missed diagnosis.
Ann Cardiol Angeiol (Paris)
; 71(2): 112-114, 2022 Apr.
Article
in En
| MEDLINE
| ID: mdl-32829892
The pulmonary alveolocapillary dysplasia (ACD) with pulmonary vein misalignment (PVM) is a rare condition characterized by a congenital anomaly of the development of the pulmonary parenchyma. We present a case of an 8-month-old infant who died quickly from acute respiratory failure complicating an unknown ACD. We also describe its epidemiological characteristics in infants and we discuss the diagnosis's difficulties. In this case, a pulmonary arterial hypertension was decompensated by an infection. A medico-legal autopsy was performed. As for the Histological examination, it showed the features of ACD/PVM.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Persistent Fetal Circulation Syndrome
/
Pulmonary Veins
Type of study:
Diagnostic_studies
/
Prognostic_studies
Limits:
Humans
/
Infant
/
Newborn
Language:
En
Journal:
Ann Cardiol Angeiol (Paris)
Year:
2022
Document type:
Article
Country of publication: