Endovascular closure of a congenital extrahepatic portosystemic shunt for the treatment of hepatopulmonary syndrome in an infant.
Pediatr Radiol
; 54(2): 357-361, 2024 02.
Article
in En
| MEDLINE
| ID: mdl-38141079
ABSTRACT
Congenital portosystemic shunts may result in the development of hepatopulmonary syndrome, typically presenting with progressive hypoxemia in later childhood. We describe a case of a 5-month-old male with heterotaxy with polysplenia presenting with new onset hypoxemia. Subsequent evaluation identified an extrahepatic portosystemic shunt arising from the confluence of the main portal and superior mesenteric veins draining into the left renal vein. To treat his hypoxemia and prevent future complications of shunting, the patient underwent a successful single-stage endovascular closure.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Portasystemic Shunt, Transjugular Intrahepatic
/
Hepatopulmonary Syndrome
/
Vascular Malformations
Limits:
Child
/
Humans
/
Infant
/
Male
Language:
En
Journal:
Pediatr Radiol
/
Pediatr. radiol
/
Pediatric radiology
Year:
2024
Document type:
Article
Affiliation country:
Country of publication: