A delayed diagnosis of Mounier-Kuhn syndrome.
BMJ Case Rep
; 20142014 Jun 02.
Article
de En
| MEDLINE
| ID: mdl-24891495
ABSTRACT
Following a provisional diagnosis of asthma of several years' duration by his general practitioner, a 43-year-old otherwise healthy man who was a non-smoker was referred to a pulmonologist with worsening productive cough and exertional breathlessness. A thoracic CT scan revealed dilated airways (tracheal diameter 35â
mm, left bronchial diameter 20â
mm, right bronchial diameter 18â
mm). Inflamed and easily collapsible airways were seen on bronchoscopy. The patient remained stable and was followed up with regular spirometry. A follow-up CT scan 7â
years later showed tracheobronchomegaly (tracheal diameter 42â
mm, left bronchial diameter 25â
mm, right bronchial diameter 23â
mm) with large cystic spaces consistent with Mounier-Kuhn syndrome. Repeat bronchoscopy showed a massively dilated trachea and generalised collapse on expiration with a dilated thin-walled bronchial tree. He was deemed ineligible for lung transplantation due to the extent of airway involvement making it difficult to anastomose donor lung to native tissue.
Texte intégral:
1
Collection:
01-internacional
Base de données:
MEDLINE
Sujet principal:
Trachéobronchomégalie
Type d'étude:
Diagnostic_studies
Limites:
Adult
/
Humans
/
Male
Langue:
En
Journal:
BMJ Case Rep
Année:
2014
Type de document:
Article
Pays d'affiliation:
Malte