Surgically treated solitary giant gluteal and retroperitoneal neurofibroma: a case report.
World J Surg Oncol
; 14: 125, 2016 Apr 27.
Article
de En
| MEDLINE
| ID: mdl-27122017
ABSTRACT
BACKGROUND:
Giant neurofibromas in patients with neurofibromatosis type 1 involve multiple regions and are often difficult to surgically extirpate. However, surgical intervention is the most effective means for improving quality of life. The case reported herein is unique in that it involves a giant neurofibroma, involving the patient's peritoneal and pelvic cavities, retroperitoneal space, and buttock, which was causing compressive displacement of abdominal and pelvic organs. A challenging surgical intervention was required to accomplish near-total resection to relieve organ compression while preserving visceral and genitoanal function. CASE PRESENTATION The case reported is of a patient presenting with a solitary giant retroperitoneal neurofibroma that threatened to obliterate both peritoneal and pelvic cavities and protruded conspicuously into the right gluteal region. The enormous dumbbell-shaped mass was surgically removed in three parts. Postoperative pathology studies confirmed a diagnosis of neurofibroma. Follow-up computed tomography images taken three months postoperatively revealed residual tumor in the perianal region. The patient's quality of life had measurably improved on follow-up at eight months.CONCLUSIONS:
Surgical intervention in such extraordinary circumstances of a giant neurofibroma causing compressive displacement of critical organs reduces tumor burden, restores appearance and function of patient's body and internal organs, and improves the patient's quality of life.Mots clés
Texte intégral:
1
Collection:
01-internacional
Base de données:
MEDLINE
Sujet principal:
Tumeurs du bassin
/
Tumeurs du rétropéritoine
/
Fesses
/
Abdomen
/
Neurofibrome
Type d'étude:
Prognostic_studies
Aspects:
Patient_preference
Limites:
Female
/
Humans
/
Middle aged
Langue:
En
Journal:
World J Surg Oncol
Année:
2016
Type de document:
Article
Pays d'affiliation:
Chine