Kaposiform hemangioendothelioma of skull base with dura invasion in a pediatric patient: a case report.
Childs Nerv Syst
; 39(11): 3289-3294, 2023 11.
Article
de En
| MEDLINE
| ID: mdl-37354290
ABSTRACT
Kaposiform hemangioendothelioma is an extremely rare vascular tumor which shows aggressive local growth. We present a case of rapid growing vascular skull tumor with dura invasion in a pediatric patient with neurofibromatosis type 1. A 14-year-old male complained of headache and dizziness for 1 month after minor head trauma. Brain magnetic resonance imaging (MRI) revealed a 5-cm-sized tumor in the left frontotemporal bone with internal hemorrhage and cystic changes. The gross total resection of tumor was done. At the 7-month follow-up, brain MRI revealed a recurrent skull tumor with intracranial dura mass. He underwent second surgery, and the pathologic diagnosis was suggestive of Kaposiform hemangioendothelioma. For this vascular proliferative tumor, mTOR inhibitor was treated for 6 months, and there was the recurred nodular-enhancing mass along the sphenoid ridge. After additional 2 months of medication, the following MRI revealed a decreased nodular-enhancing mass.
Mots clés
Texte intégral:
1
Collection:
01-internacional
Base de données:
MEDLINE
Sujet principal:
Tumeurs du crâne
/
Tumeurs vasculaires
/
Syndrome de Kasabach-Merritt
Limites:
Adolescent
/
Humans
/
Male
Langue:
En
Journal:
Childs Nerv Syst
Sujet du journal:
NEUROLOGIA
/
PEDIATRIA
Année:
2023
Type de document:
Article