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Tetralogy of Fallot with an Anomalous Course of the Brachiocephalic Vein
Matos, Larissa Alves Leite; Silva, Isaac Azevedo; Santos, Fernando Cesar Gimenes Barbosa; Croti, Ulisses Alexandre.
Affiliation
  • Matos, Larissa Alves Leite; Fundação Faculdade Regional de Medicina de São José do Rio Preto/Faculdade de Medicina de São José do Rio Preto. Hospital da Criança e Maternidade de São José do Rio Preto. Centro do Coração da Criança. São José do Rio Preto. BR
  • Silva, Isaac Azevedo; Fundação Faculdade Regional de Medicina de São José do Rio Preto/Faculdade de Medicina de São José do Rio Preto. Hospital da Criança e Maternidade de São José do Rio Preto. Centro do Coração da Criança. São José do Rio Preto. BR
  • Santos, Fernando Cesar Gimenes Barbosa; Fundação Faculdade Regional de Medicina de São José do Rio Preto/Faculdade de Medicina de São José do Rio Preto. Hospital da Criança e Maternidade de São José do Rio Preto. Centro do Coração da Criança. São José do Rio Preto. BR
  • Croti, Ulisses Alexandre; Fundação Faculdade Regional de Medicina de São José do Rio Preto/Faculdade de Medicina de São José do Rio Preto. Hospital da Criança e Maternidade de São José do Rio Preto. Centro do Coração da Criança. São José do Rio Preto. BR
Rev. bras. cir. cardiovasc ; 38(5): e20230047, 2023. tab, graf
Article in En | LILACS-Express | LILACS | ID: biblio-1449564
Responsible library: BR1.1
ABSTRACT
ABSTRACT Clinical data Infant, 11-month-old, male, diagnosis of Tetralogy of Fallot with retrotracheoesophageal course of the brachiocephalic vein. Usual findings of Tetralogy of Fallot on physical examination. Technical description Chest radiography showed slightly reduced pulmonary vascular markings and no cardiomegaly. Normal preoperative electrocardiogram with postoperative right bundle branch block. Usual findings of Tetralogy of Fallot on echocardiogram. Postoperative computed tomography angiography confirmed left brachiocephalic vein with anomalous retrotracheoesophageal course, configuring a U-shaped garland vein, in addition to postoperative findings of total correction of Tetralogy of Fallot. Operation Complete surgical repair was performed with pulmonary valve commissurotomy and placement of bovine pericardial patch to solve right ventricular outflow tract obstruction, pulmonary trunk enlargement, and ventricular septal defect closure.

Comments:

Systemic venous drainage may show variations in patients with Tetralogy of Fallot. These abnormalities are usually of little clinical relevance, as they are asymptomatic. We presented a rare case of retrotracheoesophageal course of an anomalous left brachiocephalic vein with intraoperative diagnosis, confirmed by imaging during postoperative follow-up, without compromising clinical management or surgical approach.
Key words

Full text: 1 Collection: 01-internacional Database: LILACS Language: En Journal: Rev. bras. cir. cardiovasc Journal subject: CARDIOLOGIA / CIRURGIA GERAL Year: 2023 Document type: Article Affiliation country:

Full text: 1 Collection: 01-internacional Database: LILACS Language: En Journal: Rev. bras. cir. cardiovasc Journal subject: CARDIOLOGIA / CIRURGIA GERAL Year: 2023 Document type: Article Affiliation country:
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