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Modelling urea-cycle disorder citrullinemia type 1 with disease-specific iPSCs.
Yoshitoshi-Uebayashi, Elena Yukie; Toyoda, Taro; Yasuda, Katsutaro; Kotaka, Maki; Nomoto, Keiko; Okita, Keisuke; Yasuchika, Kentaro; Okamoto, Shinya; Takubo, Noriyuki; Nishikubo, Toshiya; Soga, Tomoyoshi; Uemoto, Shinji; Osafune, Kenji.
Affiliation
  • Yoshitoshi-Uebayashi EY; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan; Department of Hepatobiliary, Pancreatic, Transplantation and Pediatric Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Toyoda T; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan.
  • Yasuda K; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan; Department of Hepatobiliary, Pancreatic, Transplantation and Pediatric Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Kotaka M; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan.
  • Nomoto K; Department of Pediatrics, Kitasato University School of Medicine, Kanagawa, Japan.
  • Okita K; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan.
  • Yasuchika K; Department of Hepatobiliary, Pancreatic, Transplantation and Pediatric Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Okamoto S; Department of Hepatobiliary, Pancreatic, Transplantation and Pediatric Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Takubo N; Department of Pediatrics and Adolescent Medicine, Juntendo University, Tokyo, Japan.
  • Nishikubo T; Department of Pediatrics, Center for Perinatal Medicine, Nara Medical University, Nara, Japan.
  • Soga T; Institute for Advanced Biosciences, Keio University, Yamagata, Japan.
  • Uemoto S; Department of Hepatobiliary, Pancreatic, Transplantation and Pediatric Surgery, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
  • Osafune K; Center for iPS Cell Research and Application (CiRA), Kyoto University, Kyoto, Japan. Electronic address: osafu@cira.kyoto-u.ac.jp.
Biochem Biophys Res Commun ; 486(3): 613-619, 2017 05 06.
Article in En | MEDLINE | ID: mdl-28302489

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Arginine / Argininosuccinate Synthase / Citric Acid Cycle / Citrullinemia / Hepatocytes / Induced Pluripotent Stem Cells Limits: Animals / Humans Language: En Journal: Biochem Biophys Res Commun Year: 2017 Document type: Article Affiliation country: Country of publication:

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Arginine / Argininosuccinate Synthase / Citric Acid Cycle / Citrullinemia / Hepatocytes / Induced Pluripotent Stem Cells Limits: Animals / Humans Language: En Journal: Biochem Biophys Res Commun Year: 2017 Document type: Article Affiliation country: Country of publication: