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Visualisation of cholesterol and ganglioside GM1 in zebrafish models of Niemann-Pick type C disease and Smith-Lemli-Opitz syndrome using light sheet microscopy.
Cook, Sophie R; Bladen, Cerys; Smith, Johanna; Maguire, Emily; Copner, Jordan; Fenn, Gareth D; Wager, Kim; Waller-Evans, Helen; Lloyd-Evans, Emyr.
Affiliation
  • Cook SR; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Bladen C; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Smith J; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Maguire E; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Copner J; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Fenn GD; Medicines Discovery Institute, Cardiff University, Main Building, Park Place, Cardiff, CF10 3AT, UK.
  • Wager K; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK.
  • Waller-Evans H; Oxford Pharmagenesis, Tubney Warren Barn, Tubney, Oxford, OX13 5QJ, UK.
  • Lloyd-Evans E; School of Biosciences, Cardiff University, Sir Martin Evans Building, Museum Avenue, Cardiff, CF10 3AX, UK. waller-evansh@cf.ac.uk.
Histochem Cell Biol ; 154(5): 565-578, 2020 Nov.
Article in En | MEDLINE | ID: mdl-33079236

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Zebrafish / Cholesterol / Smith-Lemli-Opitz Syndrome / Disease Models, Animal / Niemann-Pick Disease, Type C / G(M1) Ganglioside Type of study: Prognostic_studies Limits: Animals Language: En Journal: Histochem Cell Biol Journal subject: CITOLOGIA / HISTOCITOQUIMICA Year: 2020 Document type: Article Affiliation country:

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Zebrafish / Cholesterol / Smith-Lemli-Opitz Syndrome / Disease Models, Animal / Niemann-Pick Disease, Type C / G(M1) Ganglioside Type of study: Prognostic_studies Limits: Animals Language: En Journal: Histochem Cell Biol Journal subject: CITOLOGIA / HISTOCITOQUIMICA Year: 2020 Document type: Article Affiliation country: