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An Iron-chelating Agent Improved the Cardiac Function in a Patient with Severe Heart Failure Due to Hereditary Hemochromatosis.
Setoguchi, Akito; Kawano, Hiroaki; Okano, Shinji; Honda, Tomohiro; Kato, Takeharu; Dateki, Sumito; Senoo, Akira; Nakashima, Yomi; Motokawa, Tetsufumi; Ueno, Yuki; Akashi, Ryohei; Yonekura, Tsuyoshi; Sueyoshi, Eijun; Ikeda, Satoshi; Miyazaki, Yasushi; Maemura, Koji.
Affiliation
  • Setoguchi A; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Kawano H; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Okano S; Department of Pathology, Nagasaki University Hospital, Japan.
  • Honda T; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Kato T; Department of Hematology, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Dateki S; Department of Pediatrics, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Senoo A; Division of Electron Microscopy, Pathology and Cytology Laboratories, Japan.
  • Nakashima Y; Department of Endocrinology, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Motokawa T; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Ueno Y; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Akashi R; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Yonekura T; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Sueyoshi E; Department of Radiology, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Ikeda S; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Miyazaki Y; Department of Hematology, Nagasaki University Graduate School of Biomedical Sciences, Japan.
  • Maemura K; Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan.
Intern Med ; 63(2): 253-258, 2024 Jan 15.
Article in En | MEDLINE | ID: mdl-37197964
A 24-year-old man was admitted to our hospital because of severe heart failure. Although he was treated with diuretics and positive inotropic agents, his heart failure progressed. An endomyocardial biopsy revealed iron deposition in his myocytes. Finally, he was diagnosed with hereditary hemochromatosis. After starting administration of an iron-chelating agent in addition to conventional treatment for heart failure, his condition improved. We should consider hemochromatosis in heart failure patients with severe right ventricular dysfunction in addition to left ventricular dysfunction.
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Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Heart Failure / Hemochromatosis Limits: Adult / Humans / Male Language: En Journal: Intern Med Journal subject: MEDICINA INTERNA Year: 2024 Document type: Article Affiliation country: Country of publication:

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Heart Failure / Hemochromatosis Limits: Adult / Humans / Male Language: En Journal: Intern Med Journal subject: MEDICINA INTERNA Year: 2024 Document type: Article Affiliation country: Country of publication: