Trisomy 13 with retroiliac ureter diagnosed by assessment for recurrent febrile urinary tract infections.
IJU Case Rep
; 7(2): 161-164, 2024 Mar.
Article
in En
| MEDLINE
| ID: mdl-38440708
ABSTRACT
Introduction:
Patients with trisomy 13 have multiple malformations, including urological anomalies, and severe cognitive and psychomotor disabilities. We conducted a ureteroureterostomy for a mid-ureteral stricture due to a retroiliac ureter in a patient with trisomy 13. Case presentation A 6-month-old girl with trisomy 13 developed a urinary tract infection. Computed tomography for assessing recurrent urinary tract infection revealed a left mid-ureteral stricture due to the retroiliac ureter. At the age of 2, a ureteroureterostomy was performed. Two years after surgery, the urinary tract infection did not recur.Conclusion:
Ureteroureterostomy is a safe procedure for children with trisomy 13 and multiple comorbidities. Surgical treatment should be considered for patients with trisomy 13 when agreed upon by the family and comorbidities are well-controlled.
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Language:
En
Journal:
IJU Case Rep
Year:
2024
Document type:
Article
Country of publication: