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T-cell abnormalities in common variable immunodeficiency
Azizi, G; Rezaei, N; Kiae, F; Tavakolinia, N; Yazdani, R; Mirshafiey, A; Aghamohammadi, A.
Afiliação
  • Azizi, G; Alborz University of Medical Sciences. Imam Hassan Mojtaba Hospital. Department of Laboratory Medicine. Karaj. Iran
  • Rezaei, N; Tehran University of Medical Sciences. Research Center for Immunodeficiencies. Children’s Medical Center. Tehran. Iran
  • Kiae, F; Tehran University of Medical Sciences. Research Center for Immunodeficiencies. Children’s Medical Center. Tehran. Iran
  • Tavakolinia, N; Tehran University of Medical Sciences. Research Center for Immunodeficiencies. Children’s Medical Center. Tehran. Iran
  • Yazdani, R; Isfahan University of Medical Sciences. School of Medicine. Department of Immunology. Isfahan. Iran
  • Mirshafiey, A; Tehran University of Medical Sciences. School of Public Health. Department of Immunology. Tehran. Iran
  • Aghamohammadi, A; Tehran University of Medical Sciences. Research Center for Immunodeficiencies. Children’s Medical Center. Tehran. Iran
J. investig. allergol. clin. immunol ; 26(4): 233-243, 2016. tab
Artigo em Inglês | IBECS | ID: ibc-154935
Biblioteca responsável: ES1.1
Localização: BNCS
ABSTRACT
Common variable immunodeficiency (CVID) is the most common clinical primary immunodeficiency. It is characterized by a defect in B-cell differentiation to plasma and memory B cells. Moreover, numerous T-cell abnormalities have been reported and include decreased T-cell count and proliferative response, increased T-cell activation and apoptosis, and abnormalities in cytokine production. The aims of this review are to describe phenotypic and functional defects in T cells in CVID patients and to review the literature with respect to the effects of immunoglobulin replacement on the T-cell component in CVID patients (AU)
RESUMEN
La inmunodeficiencia común variable (CVID) es la inmunodeficiencia primaria más frecuente. Se caracteriza por un defecto en la diferenciación de linfocitos B hacia células plasmáticas y linfocitos B memoria. Se han descrito numerosas alteraciones en los linfocitos T de estos pacientes, tales como disminución en el número de linfocitos T y en sus respuestas proliferativas, aumento en la activación de células T y en la apoptosis, así como alteraciones en la producción de citokinas. El objetivo de esta revisión es describir las alteraciones funcionales y fenotípicas de los linfocitos T en los pacientes con CVID y revisar la bibliografía en relación a los efectos que la administración de inmunoglobulinas produce en los linfocitos T de los pacientes con CVID (AU)
Assuntos

Texto completo: Disponível Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Plasmócitos / Linfócitos B / Linfócitos T / Imunodeficiência de Variável Comum / Linfócitos T Reguladores Limite: Feminino / Humanos / Masculino Idioma: Inglês Revista: J. investig. allergol. clin. immunol Ano de publicação: 2016 Tipo de documento: Artigo Instituição/País de afiliação: Alborz University of Medical Sciences/Iran / Isfahan University of Medical Sciences/Iran / Tehran University of Medical Sciences/Iran

Texto completo: Disponível Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Plasmócitos / Linfócitos B / Linfócitos T / Imunodeficiência de Variável Comum / Linfócitos T Reguladores Limite: Feminino / Humanos / Masculino Idioma: Inglês Revista: J. investig. allergol. clin. immunol Ano de publicação: 2016 Tipo de documento: Artigo Instituição/País de afiliação: Alborz University of Medical Sciences/Iran / Isfahan University of Medical Sciences/Iran / Tehran University of Medical Sciences/Iran
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