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Impact of rare diseases in oral health
Molina García, Ana; Castellanos Cosano, Lizett; Machuca Portillo, Guillermo; Posada de la Paz, Manuel.
Afiliação
  • Molina García, Ana; University of Seville. Seville. Spain
  • Castellanos Cosano, Lizett; University of Seville. Department of Stomatology. Seville. Spain
  • Machuca Portillo, Guillermo; University of Seville. Department of Stomatology. Seville. Spain
  • Posada de la Paz, Manuel; Health Institute Carlos III. Rare Diseases Research. Madrid. Spain
Med. oral patol. oral cir. bucal (Internet) ; 21(5): e587-e594, sept. 2016. tab, graf
Artigo em Inglês | IBECS | ID: ibc-155770
Biblioteca responsável: ES1.1
Localização: BNCS
ABSTRACT

BACKGROUND:

Rare diseases (RD) are those that present a lower prevalence than 5 cases per 10.000 population. The main objective of this review was to study the effect on oral health in rare diseases, while the secondary objective of the study is theme upgrade. MATERIAL AND

METHODS:

Comparative observational case-control studies were analysed and a systematic review was conducted in PubMed. Each rare disease listed on the statistical data record of the Health Portal of the Ministry of Equality, Health and Social Policies Board of Andalusia was associated with 'oral health'. The variables studied included dental, oral mucosa and occlusion alterations, oral pathologies (caries, periodontal disease) and other alterations (mouth breathing, parafunctional habits, etc). A bias analysis of the variable caries was conducted.

RESULTS:

Six RD were selected through our inclusion and exclusion criteria (hypogammaglobulinemia, Rett syndrome, Marfan syndrome, Prader-Willi syndrome, cystic fibrosis and Cri du chat syndrome) in a total of 8 publications, of which four trials were classified as high risk of bias and one of them as medium risk. There were not trials with low risk of bias.

CONCLUSIONS:

The main statistically significant differences found by Syndrome compared to a control group were in Hypogammaglobulinemia with a greater tendency to enamel hypoplasia and dry mouth. The Rett syndrome had, as well, a greater tendency to an anterior open bite, ogival palate, bruxism, mouth breathing and tongue thrusting. Prader-Willi syndrome had a tendency of dental erosion, and Cri du chat syndrome showed a higher association to Tannerella forsythia
Assuntos

Texto completo: Disponível Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Doenças Raras / Doenças da Boca Tipo de estudo: Estudo observacional / Fatores de risco Limite: Humanos Idioma: Inglês Revista: Med. oral patol. oral cir. bucal (Internet) Ano de publicação: 2016 Tipo de documento: Artigo Instituição/País de afiliação: Health Institute Carlos III/Spain / University of Seville/Spain

Texto completo: Disponível Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Doenças Raras / Doenças da Boca Tipo de estudo: Estudo observacional / Fatores de risco Limite: Humanos Idioma: Inglês Revista: Med. oral patol. oral cir. bucal (Internet) Ano de publicação: 2016 Tipo de documento: Artigo Instituição/País de afiliação: Health Institute Carlos III/Spain / University of Seville/Spain
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