Histiocitosis congénita autolimitada: a propósito de un caso / Congenital self-healing histiocytosis: A case report
Acta pediatr. esp
; 77(3/4): e53-e56, mar.-abr. 2019. ilus
Artigo
em Espanhol
| IBECS
| ID: ibc-188583
Biblioteca responsável:
ES1.1
Localização: BNCS
RESUMEN
Introducción:
La histiocitosis/reticulohistiocitosis congénita autolimitada (HCAL) es una variante infrecuente de histiocitosis de células de Langerhans presente de forma congénita o neonatal, de etiología desconocida. La presentación usualmente es múltiple, aunque en un 25% de los casos es solitaria. Caso clínico Presentamos el caso de un neonato con una lesión localizada en el abdomen, caracterizada por una úlcera de 1 cm, cubierta por una costra amarilla-marrón fibrinoide con un borde bien definido, eritematoso y sobreelevado. El paciente presentaba un excelente estado general, sin otras lesiones ni presencia de adenopatías o visceromegalias. Se indicaron estudios para descartar una patología infecciosa y se realizó una biopsia cutánea. El estudio histopatológico e inmunohistoquímico confirmó el diagnóstico de HCAL.Resultados:
Se descartaron lesiones extracutáneas. La lesión involucionó sin requerir tratamiento, resolviéndose de manera satisfactoria en 3 meses, sin afectación extracutánea hasta la fechaABSTRACT
Introduction:
Congenital self-healing histiocytosis/reticulohistiocytosis (CSHH) is an infrequent variant of Langerhans cell histiocytosis present congenitally or neonatally. Etiology is unknown. The presentation is usually multiple, however in 25% of the cases the appearance would be solitary. Case report We present the case of a neonate with a lesion located in the abdomen, characterized by a 1 cm ulcer, covered by a yellow-brown fibrinoid scab with a well-defined, erythematous and raised border. The patient was in excellent general condition, without other lesions, or the presence of lymphadenopathy or visceromegaly. Studies were indicated to rule out infectious pathology and a skin biopsy was performed. The histopathological and immunohistochemical study confirmed the diagnosis of CSHH.Results:
Extracutaneous lesions were ruled out. The lesion involuted without requiring treatment resolving satisfactorily in 3 months, without extracutaneous commitment to date
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Coleções:
Bases de dados nacionais
/
Espanha
Base de dados:
IBECS
Assunto principal:
Úlcera Cutânea
/
Histiocitose
/
Histiocitose de Células de Langerhans
Limite:
Humanos
/
Masculino
/
Recém-Nascido
Idioma:
Espanhol
Revista:
Acta pediatr. esp
Ano de publicação:
2019
Tipo de documento:
Artigo
Instituição/País de afiliação:
Centro Hospitalario Pereira/Uruguay