Crossed hemi-hyperplasia with hemi-megalencephaly - An unusualsyndromic presentation

ABSTRACT

Hemimegalencephaly is a rare disorder which may present alone or be associated with hemicorporal gigantism. However, an association with crossed hemicorporal gigantism involving different upper and lower halves of the body along with selective visceromegaly is, so far, unreported in literature.A 14-year-old male presented with a crossed variety of hemigigantism associated with a mild form of hemimegalencephaly affecting the left cer-ebral and cerebellar hemispheres. On ultrasound, left renomegaly was noted, though no pathology or dysfunction of the organ could be demonstrated. This case merited a report due to an unusual presentation that defies explanations offered so far for the condition

RESUMEN

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