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Sphenoidal meningoencephalocele associated with CSF fistula and arteriovenous malformation Spetzler-Martin V: A case report / Meningoencefalocele esfenoidal asociado a fístula de líquido cefalorraquídeo y malformación arteriovenosa Spetzler-Martin V: reporte de caso
Ramírez-Ferrer, Esteban; Aponte-Caballero, Rafael; Aguilera-Pena, Maria Paula; Mendoza-Ayús, Santiago David; Osorio-Bohorquez, Luis Alejandro; Riveros-Castillo, William Mauricio.
Afiliação
  • Ramírez-Ferrer, Esteban; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
  • Aponte-Caballero, Rafael; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
  • Aguilera-Pena, Maria Paula; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
  • Mendoza-Ayús, Santiago David; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
  • Osorio-Bohorquez, Luis Alejandro; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
  • Riveros-Castillo, William Mauricio; Rosario University School of Medicine. Samaritan University Hospital. Center for Research and Training in Neurosurgery (CIEN). Bogotá. Colombia
Neurocirugía (Soc. Luso-Esp. Neurocir.) ; 34(2): 93-96, mar.-abr. 2023. ilus
Artigo em Inglês | IBECS | ID: ibc-217070
Biblioteca responsável: ES1.1
Localização: ES15.1 - BNCS
ABSTRACT
Cerebral Arteriovenous malformations (AVMs) are presumed congenital anomalies of the blood vessels, which can increase intracranial pressure by uncertain mechanisms. We report the rare case of a 55-year-old male patient who complained about CSF rhinorrhea. Persisting CSF leakage prompted CT, which evidenced a bone defect in the right middle cranial fossa with protruding brain tissue. The diagnosis of a sphenoidal meningoencephalocele was made. Neuroimaging evidenced an AVM Spetzler Martin V. The lesion was targeted via an endonasal approach with resection of the herniated brain tissue and closure of the bony and dural defects. The postoperative course was uneventful without recurrence of the CSF fistula. Documentation of these cases is essential to come up with standardized therapeutical protocols and follow-up. Nevertheless, conservative management of the AVM and surgical repair of the bone defects is an appropriate approach in the first instance, depending on the morphology and characterization of the AVM (AU)
RESUMEN
Las malformaciones arteriovenosas (MAV) son consideradas anomalías congénitas de los vasos sanguíneos; estas pueden aumentar la presión intracraneal a través de mecanismos inciertos. Reportamos el caso de un hombre de 55 años con presencia de rinolicuorrea de larga data. Se realizó la toma de una TC de cráneo, evidenciando un defecto óseo en la fosa craneal media derecha con protrusión de tejido cerebral, diagnosticando un meningoencefalocele esfenoidal. Las imágenes complementarias evidenciaron una MAV Spetzler-Martin V. La lesión fue tratada con un abordaje endonasal resecando el tejido cerebral herniado con cierre de los defectos dural y óseo. En el postoperatorio no hubo recurrencia de rinolicuorrea. La documentación de estos casos es esencial para generar protocolos estandarizados de tratamiento y seguimiento. En nuestra experiencia el manejo conservador de la MAV y el reparo quirúrgico de los defectos es un abordaje adecuado, teniendo en cuenta la morfología y caracterización de la MAV (AU)
Assuntos

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Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Malformações Arteriovenosas Intracranianas / Rinorreia de Líquido Cefalorraquidiano / Meningocele Limite: Humanos / Masculino Idioma: Inglês Revista: Neurocirugía (Soc. Luso-Esp. Neurocir.) Ano de publicação: 2023 Tipo de documento: Artigo Instituição/País de afiliação: Rosario University School of Medicine/Colombia
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Coleções: Bases de dados nacionais / Espanha Base de dados: IBECS Assunto principal: Malformações Arteriovenosas Intracranianas / Rinorreia de Líquido Cefalorraquidiano / Meningocele Limite: Humanos / Masculino Idioma: Inglês Revista: Neurocirugía (Soc. Luso-Esp. Neurocir.) Ano de publicação: 2023 Tipo de documento: Artigo Instituição/País de afiliação: Rosario University School of Medicine/Colombia
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