Your browser doesn't support javascript.
loading
Dermatomyositis: analysis of 109 patients surveyed at the Hospital das Clínicas (HCFMUSP), São Paulo, Brazil
Ortigosa, Luciena Cegatto Martins; Reis, Vitor Manuel Silva dos.
Afiliação
  • Ortigosa, Luciena Cegatto Martins; Universidade de São Paulo. São Paulo. BR
  • Reis, Vitor Manuel Silva dos; Universidade de São Paulo. São Paulo. BR
An. bras. dermatol ; 89(5): 719-727, Sep-Oct/2014. tab, graf
Artigo em Inglês | LILACS | ID: lil-720803
Biblioteca responsável: BR1.1
ABSTRACT

BACKGROUND:

Dermatomyositis affects striated muscles, skin and other organs.

OBJECTIVE:

To characterize the disease from January 1992 to December 2002, assessing its classification, cutaneous and systemic manifestations, and also laboratory results, therapeutic and prognostic findings compared to those in the literature.

METHODS:

Data were obtained from medical records of 109 patients who were classified into five groups 23 juvenile dermatomyositis; 59 primary idiopathic dermatomyositis; 6 amyopathic dermatomyositis; 7 dermatomyositis associated with neoplasms and 14 dermatomyositis associated with other connective tissue diseases.

RESULTS:

Sixty patients were classified as "definite" diagnosis; 33 as "possible"; four as "probable" and 12 and as amyopathic. The average age at diagnosis was 36 years. Cutaneous manifestations occurred in all patients; the most frequent symptom was loss of proximal muscle strength; the most common pulmonary disorder was interstitial lung disease, and gastritis was the most prevalent digestive manifestation. Tumors were documented in 6.42% of cases. Lactate dehydrogenase was the muscle enzyme most frequently elevated in the majority of cases. Skin biopsies were performed in 68 patients; muscle biopsies in 53; and electroneuromyographies in 58 patients. The most commonly used treatment was corticotherapy and the mortality rate was 14.7%.

CONCLUSION:

in this sample, the disease appeared in younger individuals, was more frequent in women and the association with cancer was small. .
Assuntos


Texto completo: Disponível Coleções: Bases de dados internacionais Base de dados: LILACS Assunto principal: Dermatomiosite Tipo de estudo: Estudo prognóstico Limite: Adolescente / Adulto / Idoso / Idoso, 80 anos ou mais / Criança / Criança, pré-escolar / Feminino / Humanos / Masculino País/Região como assunto: América do Sul / Brasil Idioma: Inglês Revista: An. bras. dermatol Assunto da revista: Dermatologia Ano de publicação: 2014 Tipo de documento: Artigo País de afiliação: Brasil Instituição/País de afiliação: Universidade de São Paulo/BR

Texto completo: Disponível Coleções: Bases de dados internacionais Base de dados: LILACS Assunto principal: Dermatomiosite Tipo de estudo: Estudo prognóstico Limite: Adolescente / Adulto / Idoso / Idoso, 80 anos ou mais / Criança / Criança, pré-escolar / Feminino / Humanos / Masculino País/Região como assunto: América do Sul / Brasil Idioma: Inglês Revista: An. bras. dermatol Assunto da revista: Dermatologia Ano de publicação: 2014 Tipo de documento: Artigo País de afiliação: Brasil Instituição/País de afiliação: Universidade de São Paulo/BR
...