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A Rare Case Report of Inguinal Hernia with Persistent Mullerian Duct and Klinefelter Syndrome.
J Clin Diagn Res ; 10(6): PD28-9, 2016 Jun.
Artigo em Inglês | MEDLINE | ID: mdl-27504355
Inguinal hernia in male is a common problem but having female reproductive organs in hernial sac is rare. It occur because of failure of mullerian duct to regress in a male fetus during embryonic development, result in a syndrome known as Persistent Mullerian Duct Syndrome (PMDS), which is a rare entity of male pseudohermaphroditism. We hereby present a case of 21-year-old male patient reported with complains of cryptorchidism and inguinal hernia. Generally diagnosis of PMDS was established during investigation like ultrasonography, MRI for localization of undescended testis and during surgical exploration for inguinal hernia or cryptorchidism. Our patient was operated by bilateral inguinal incision; hernial sac contained adult size uterus fallopian tube and upper 2/3(rd) of vagina. On karyotyping it was found that he was a case of klinefelter syndrome also. Association of PMDS with klinefelter syndrome is very rare.





Texto completo: Disponível Coleções: Bases de dados internacionais Base de dados: MEDLINE Tipo de estudo: Relato de casos Idioma: Inglês Revista: J Clin Diagn Res Ano de publicação: 2016 Tipo de documento: Artigo País de afiliação: Índia