Tratamiento con sirolimus y prednisona en enfermedad de Erdheim-Chester con compromiso cardiaco: caso clínico / Sirolimus and prednisone for the treatment of Erdheim-Chester disease with cardiac involvement: report of one case
Rev. méd. Chile
; 144(3): 394-400, mar. 2016. ilus, tab
Article
em Es
| LILACS
| ID: lil-784911
Biblioteca responsável:
CL1.1
ABSTRACT
Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytic disorder. We report a 76-years-old man who suffered a cardiac tamponade secondary to ECD. A pericardial window was made and during the operation the surgeons observed that the myocardium was diffusely infiltrated. Twenty-eight months before, ECD was clinically diagnosed and prednisone and methotrexate were prescribed. Due to disease progression which culminated in the cardiac tamponade, methotrexate was changed to sirolimus aiming to obtain plasma levels between 5-8 ng/ml. This treatment stabilized his cardiac function allowing a survival of 52 months after its initiation, with fewer side effects.
Palavras-chave
Texto completo:
1
Temas:
Saude_idoso
Base de dados:
LILACS
Assunto principal:
Prednisona
/
Tamponamento Cardíaco
/
Sirolimo
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Doença de Erdheim-Chester
/
Anti-Inflamatórios
Idioma:
Es
Revista:
Rev. méd. Chile
Assunto da revista:
MEDICINA
Ano de publicação:
2016
Tipo de documento:
Article
País de afiliação:
Chile