Detalhe da pesquisa
1.
Therapeutic Small Interfering RNA Targeting Complement C3 in a Mouse Model of C3 Glomerulopathy.
J Immunol
; 208(7): 1772-1781, 2022 04 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-35277417
2.
Anti-CFH-associated hemolytic uremic syndrome: do we still need plasma exchange?
Pediatr Nephrol
; 2024 Apr 17.
Artigo
em Inglês
| MEDLINE | ID: mdl-38632123
3.
An Ex Vivo Test of Complement Activation on Endothelium for Individualized Eculizumab Therapy in Hemolytic Uremic Syndrome.
Am J Kidney Dis
; 74(1): 56-72, 2019 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-30851964
4.
Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.
J Immunol
; 199(3): 1021-1040, 2017 08 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-28652401
5.
Autoimmune abnormalities of the alternative complement pathway in membranoproliferative glomerulonephritis and C3 glomerulopathy.
Pediatr Nephrol
; 34(8): 1311-1323, 2019 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-29948306
6.
Withdrawals/Retractions: Insights into the effects of complement factor H on the assembly and decay of the alternative pathway C3 proconvertase and C3 convertase.
J Biol Chem
; 292(15): 6094, 2017 04 14.
Artigo
em Inglês
| MEDLINE | ID: mdl-28411212
7.
Insights into the Effects of Complement Factor H on the Assembly and Decay of the Alternative Pathway C3 Proconvertase and C3 Convertase.
J Biol Chem
; 291(15): 8214-30, 2016 Apr 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-26903516
8.
Dynamics of complement activation in aHUS and how to monitor eculizumab therapy.
Blood
; 124(11): 1715-26, 2014 Sep 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-25037630
9.
Complement factor B mutations in atypical hemolytic uremic syndrome-disease-relevant or benign?
J Am Soc Nephrol
; 25(9): 2053-65, 2014 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-24652797
10.
MYO1E mutations and childhood familial focal segmental glomerulosclerosis.
N Engl J Med
; 365(4): 295-306, 2011 Jul 28.
Artigo
em Inglês
| MEDLINE | ID: mdl-21756023
11.
Residual plasmatic activity of ADAMTS13 is correlated with phenotype severity in congenital thrombotic thrombocytopenic purpura.
Blood
; 120(2): 440-8, 2012 Jul 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-22529288
12.
HUS and TTP: traversing the disease and the age spectrum.
Semin Nephrol
; 43(4): 151436, 2023 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-37949684
13.
Liver factor B silencing to cure C3 glomerulopathy: Evidence from a mouse model of complement dysregulation.
Mol Immunol
; 161: 25-32, 2023 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-37481826
14.
Mutation Analysis of PKD1 and PKD2 Genes in a Large Italian Cohort Reveals Novel Pathogenic Variants Including A Novel Complex Rearrangement.
Nephron
; 2023 May 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-37231942
15.
SARS-CoV-2 Spike Protein 1 Activates Microvascular Endothelial Cells and Complement System Leading to Platelet Aggregation.
Front Immunol
; 13: 827146, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-35320941
16.
Mycoplasma pneumoniae Infection Associated with Anti-Factor H Autoantibodies in Atypical Hemolytic Uremic Syndrome.
Nephron
; 146(6): 593-598, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-35405682
17.
CFH and CFHR structural variants in atypical Hemolytic Uremic Syndrome: Prevalence, genomic characterization and impact on outcome.
Front Immunol
; 13: 1011580, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-36793547
18.
Mutations in FN1 cause glomerulopathy with fibronectin deposits.
Proc Natl Acad Sci U S A
; 105(7): 2538-43, 2008 Feb 19.
Artigo
em Inglês
| MEDLINE | ID: mdl-18268355
19.
Amnion epithelial cells are an effective source of factor H and prevent kidney complement deposition in factor H-deficient mice.
Stem Cell Res Ther
; 12(1): 332, 2021 06 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-34112227
20.
CFH and CFHR Copy Number Variations in C3 Glomerulopathy and Immune Complex-Mediated Membranoproliferative Glomerulonephritis.
Front Genet
; 12: 670727, 2021.
Artigo
em Inglês
| MEDLINE | ID: mdl-34211499