Unilateral agenesis of the abdominal wall musculature: An early muscle deficiency.

Prune-belly sequence (PBS) usually results from early urethral obstruction. In rare cases, PBS seems to be due to a faulty primary development of the parietal mesenchyme leading to underdevelopment of the abdominal wall musculature, and disorganization of the smooth muscles in the urinary tract. We report on two patients with segmental, unilateral wall musculature deficiency associated with homolateral agenesis of ribs. One patient also had hemivertebrae and the other one ipsilateral diaphragmatic eventration and aplasia cutis. This combination of anomalies may represent a localized deficiency in the development of somitic mesoderm mesenchyme during early embryogenesis.

[Transverse testicular ectopia in children: a case report]. / L'ectopie testiculaire transverse de l'enfant: à propos d'un cas.

Transverse testicular ectopia is a rare abnormality of testicular migration in children. However, it must be suspected and investigated in any child with inguinal hernia associated with non-palpable contralateral cryptorchidism to ensure appropriate management, after eliminating, in particular persistent Müllerian duct syndrome.