Pediatric Plexiform Fibromyxoma: A Case Report.

The plexiform fibromyxoma is a rare mesenchymal tumor in adults that generally originates in the antrum of stomach, being its occurrence in pediatric patients exceptional. It was classified as a distinct entity by World Health Organization in 2010. No recurrences and metastases have been documented in many of the reported patients to date, being the surgical treatment curative. We report the case of a 3-month-old infant who presented to the emergency department with an episode of intestinal subocclusion requiring an emergent surgery. During the surgical intervention, a mass was identified in the jejunum, causing partial occlusion of its lumen. The surgical pathology report revealed an infiltrative tumor composed of spindle-shaped cells disposed in a stroma with a plexiform pattern alternating myxoid areas. These findings and the immunohistochemical characteristics of the neoplastic cells led to classify the tumor as a plexiform fibromyxoma. A description of the immunophenotype of this tumor is made and differential diagnosis with other gastrointestinal tumors is also discussed.

Aspiració de cossos estranys: la nostra experiència / Foreign body aspiration: the experience of a single institution

Fonament. L'aspiració de cossos estranys és una patologiad'elevada incidència a l'edat pediàtrica, i té greuscomplicacions si passa desprevinguda.Objectiu. Analitzar els registres dels pacients ambsospita d'aspiració de cossos estranys, i intentar obtenirconclusions per millorar el diagnòstic i el maneig d'aquestspacients.Mètode. S'ha fet un estudi retrospectiu dels 68 infantsals quals es va fer una broncoscòpia sota l'orientaciódiagnòstica d'aspiració de cos estrany, entre gener de 1998i juny de 2002, analitzant les variables demogràfiques elementalsi les característiques més significatives de la històriaclínica i l'evolució.Resultats. L'edat mitjana dels pacients va ser de 2,85anys. La simptomatologia més freqüent va ser la tos. El91.2% dels casos presentava un antecedent d'ennuegada.La majoria eren fruits secs (82.3%). El temps mitjà d'evolucióva ser de 8.96 dies.Conclusions. Els avenços tècnics han permès millorarel tractament, però el diagnòstic continua basant-se ambl'anamnesi, l'exploració i la sospita clínica. La prevenció ésla mesura fonamental per millorar el maneig d'aquestaentitat

Background. Foreign body aspiration is commonin children, and may have important consequences ifundiagnosed.Objective. To review our experience with the evaluationof patients with a suspected foreign body aspiration,and to develop guidelines to improve diagnosis and treatment.Method. Retrospective study including children whounderwent a bronchoscopy for the presumptive diagnosisof aspiration of a foreign body, between January 1998 andJune 2002.Results. Sixty-eigh patients (median age 2.85 years)were identified. The most common symptom was cough.In 91.2% of the cases there was history of chocking. Inmost cases (82.3%), the foreign body was a nut. The mediantime of symptoms was 8.96 days.Conclusions. New technologies have contributed toimproved treatments, but the most important diagnostictools remain the clinical history, physical examination, andthe high level of suspicion; preventive measures are critical