RESUMO
BACKGROUND: There is limited information regarding early development of soft-tissue and/or bone hypertrophy with facial port-wine stains (PWS). OBJECTIVE: We sought to characterize patients with hypertrophic PWS presenting during childhood. METHODS: Patients with a facial PWS and underlying hypertrophy that developed before the age of 18 years were included in a multicenter retrospective study. Age at onset of the hypertrophy, its location, association with odontologic problems, presence of other associated complications, and response to laser treatment were recorded. RESULTS: A total of 98 patients were included. The mean age at onset of hypertrophy, retrieved for 77 of 98 patients, was 5.6 years. The hypertrophy was congenital in 26%. Odontologic problems were noted in 39.8% of cases. Other complications, including cataract, asymmetric development of the maxillary bone, and speech delay/disorders, were reported in 18.4%. In all, 67 patients received laser treatment. Only 3% achieved complete or nearly complete clearance of the PWS. LIMITATIONS: As only cases of PWS with early-onset hypertrophy were included, we were unable to calculate the prevalence of this manifestation. CONCLUSION: PWS with early-onset hypertrophy are associated with a high rate of complications and a poor response to laser treatment. Periodic monitoring is recommended for early detection and treatment of complications.
Assuntos
Anormalidades Múltiplas , Lasers de Corante/uso terapêutico , Mancha Vinho do Porto/patologia , Mancha Vinho do Porto/cirurgia , Anormalidades Múltiplas/diagnóstico , Adolescente , Adulto , Idoso , Idoso de 80 Anos ou mais , Criança , Pré-Escolar , Face , Feminino , Humanos , Hipertrofia/congênito , Hipertrofia/patologia , Hipertrofia/cirurgia , Lactente , Masculino , Pessoa de Meia-Idade , Pescoço , Mancha Vinho do Porto/complicações , Prognóstico , Estudos Retrospectivos , Adulto JovemRESUMO
Teaching Point: Carcinoid tumors can release hormones responsible of cardiac valves fibrosis known as carcinoid heart disease.
RESUMO
Teaching point: Careful analysis of tubes positioning on chest X-ray not only reveals misplacement but also helps to plan a safe removal.