Detalhe da pesquisa
1.
A randomized trial of oral prednisone for cystic fibrosis pulmonary exacerbation treatment.
Eur Respir J
; 2024 May 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-38697648
2.
Phase 3 Open-Label Clinical Trial of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged 2-5 Years with Cystic Fibrosis and at Least One F508del Allele.
Am J Respir Crit Care Med
; 208(1): 59-67, 2023 07 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-36921081
3.
Long-Term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged ⩾6 Years with Cystic Fibrosis and at Least One F508del Allele: A Phase 3, Open-Label Clinical Trial.
Am J Respir Crit Care Med
; 208(1): 68-78, 2023 07 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37154609
4.
Brain AVM compactness score in children with hereditary hemorrhagic telangiectasia.
Childs Nerv Syst
; 2024 Mar 22.
Artigo
em Inglês
| MEDLINE | ID: mdl-38517485
5.
Evaluation of clinically relevant changes in the lung clearance index in children with cystic fibrosis and healthy controls.
Thorax
; 78(4): 362-367, 2023 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-35428702
6.
A 3D stack-of-spirals approach for rapid hyperpolarized 129 Xe ventilation mapping in pediatric cystic fibrosis lung disease.
Magn Reson Med
; 89(3): 1083-1091, 2023 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-36433705
7.
Inter- and intravisit repeatability of free-breathing MRI in pediatric cystic fibrosis lung disease.
Magn Reson Med
; 89(5): 2048-2061, 2023 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-36576212
8.
Longitudinal Assessment of Curaçao Criteria in Children with Hereditary Hemorrhagic Telangiectasia.
J Pediatr
; 263: 113665, 2023 Dec.
Artigo
em Inglês
| MEDLINE | ID: mdl-37572862
9.
Intra- and Inter-visit Repeatability of 129 Xenon Multiple-Breath Washout MRI in Children With Stable Cystic Fibrosis Lung Disease.
J Magn Reson Imaging
; 58(3): 936-948, 2023 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-36786650
10.
Clinical Effectiveness of Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis: A Clinical Trial.
Am J Respir Crit Care Med
; 205(5): 529-539, 2022 03 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34784492
11.
Efficacy and Safety of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 Through 11 Years of Age with Cystic Fibrosis Heterozygous for F508del and a Minimal Function Mutation: A Phase 3b, Randomized, Placebo-controlled Study.
Am J Respir Crit Care Med
; 206(11): 1361-1369, 2022 12 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-35816621
12.
Lower Airway Nitrogen Oxide Levels in Children with Primary Ciliary Dyskinesia Is Linked to Neutrophilic Inflammation.
J Pediatr
; 244: 230-233, 2022 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-35120987
13.
Lung Clearance Index to Track Acute Respiratory Events in School-Age Children with Cystic Fibrosis.
Am J Respir Crit Care Med
; 203(8): 977-986, 2021 04 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-33030967
14.
Cystic Fibrosis.
N Engl J Med
; 389(18): 1693-1707, 2023 Nov 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-37913507
15.
Time to get serious about the detection and monitoring of early lung disease in cystic fibrosis.
Thorax
; 76(12): 1255-1265, 2021 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-33927017
16.
Unsupervised phenotypic clustering for determining clinical status in children with cystic fibrosis.
Eur Respir J
; 58(2)2021 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-33446607
17.
Determinants of lung disease progression measured by lung clearance index in children with cystic fibrosis.
Eur Respir J
; 58(1)2021 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-33542049
18.
Second International Guidelines for the Diagnosis and Management of Hereditary Hemorrhagic Telangiectasia.
Ann Intern Med
; 173(12): 989-1001, 2020 12 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-32894695
19.
Primary care providers' role in newborn screening result notification for cystic fibrosis.
Can Fam Physician
; 67(6): 439-448, 2021 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-34127469
20.
Newborn screening for cystic fibrosis: Role of primary care providers in caring for infants with positive screening results.
Can Fam Physician
; 67(6): e144-e152, 2021 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-34127476