RESUMO
Madelung disease is rare, and characterised by accumulation of fatty non-encapsulated tissue in the head, neck, shoulders, and upper extremities. The aetiology is not completely known, but the association with alcohol intake is clear. We present a neglected case that was associated with bilateral asymmetrical gynaecomastia. To the best of our knowledge, this is a pattern of involvement not previously reported. The treatment of choice is lipectomy for severe cases and liposuction for less extensive accumulations of fat.
Assuntos
Doenças dos Genitais Masculinos/diagnóstico , Ginecomastia/diagnóstico , Lipomatose Simétrica Múltipla/diagnóstico , Escroto/fisiopatologia , Alcoolismo/complicações , Alcoolismo/diagnóstico , Seguimentos , Doenças dos Genitais Masculinos/complicações , Ginecomastia/complicações , Ginecomastia/cirurgia , Humanos , Lipectomia/métodos , Lipomatose Simétrica Múltipla/complicações , Lipomatose Simétrica Múltipla/cirurgia , Masculino , Mastectomia/métodos , Pessoa de Meia-Idade , Doenças Raras , Medição de Risco , Índice de Gravidade de Doença , Fumar/efeitos adversos , Resultado do TratamentoRESUMO
PURPOSE: This case report describes a rare and aggressive ameloblastic carcinoma that infiltrated the mandible in a "honeycomb" pattern. METHODS: A total mandibulectomy with bilateral modified neck dissection was followed by primary reconstruction with a single free vascularised fibula flap. RESULTS: The postoperative course was uneventful. The one year follow-up revealed no signs of recurrent tumour or metastases. Nine months later distant metastases occurred in the lung. CONCLUSION: Ameloblastic carcinoma is a highly malignant lesion, which requires aggressive therapy. Prognosis is poor. Further reporting of ameloblastic carcinoma is encouraged.