Inflammatory myofibroblastic tumor of the lacrimal gland: case report of an exceptional location.

BACKGROUND: Inflammatory myofibroblastic tumour (IMT) is a mesenchymal neoplasm of intermediate biological potential that may affect a wide range of anatomic sites but has a particular predilection for the lung and intra-abdominal soft tissues. CASE PRESENTATION: We report here an exceptional case of inflammatory myofibroblastic tumor arising in the lacrimal gland and presenting as an orbital mass in a 24-year-old male. CONCLUSION: This report aims to discuss the importance of histopathological and immunohistochemical findings in arriving at the diagnosis, which helps dictate the management, treatment and prognosis of the patient.

Association of Sweet's Syndrome and Behçet's Disease: Is It Possible? A Case Report.

Introduction: Behçet's disease is a systemic vasculitis characterized by a large clinical polymorphism with a particular frequency of cutaneous signs. Sweet's syndrome is a neutrophilic dermatosis marked by the sudden appearance of painful skin lesions in the form of erythematous papules, nodules or plaques. This syndrome is associated with high fever, neutrophilia and histologically a diffuse infiltrate of neutrophils in the dermis. Observation: We report the case of a 43-year-old patient followed for Behçet's disease, who developed cutaneous plaques of neutrophilic dermatosis of both upper limbs. The clinical and biological picture was in favor of Sweet's syndrome. Conclusion: The coexistence of Sweet's syndrome and Behçet's disease is already reported in the literature. The association is however very rare given the differences in the clinical and pathogenic features between the two conditions. LEARNING POINTS: The appearance of neutrophilic dermatosis during a skin flare-up of Behçet's disease alerted us to a possible link between Sweet's syndrome and Behçet's disease.The morphology of the skin lesions associated with these pathologies is heterogeneous, making diagnosis sometimes difficult.Cases reported in the literature concerning the association between Sweet's syndrome and Behçet's disease are rare.

Splenic metastasis from neuroendocrine tumor of the stomach: A case report.

Splenic metastasis is extremely rare, and neuroendocrine tumor of the stomach represents one of the rarest primary sources. The present study aimed to describe a rare case of an endocrine tumor of the stomach revealed by a splenic metastasis. We report a rare case of a 40 -year-old who presented a pain in her left hypochondriac, associated to sensation of heaviness. Abdominal ultrasound showed splenomegaly with a large lobulated hyperechoic mass associated to splenic vein thrombosis. A magnetic resonance imaging (MRI) confirming the splenomegaly, containing a large lobulated and heterogeneous mass occupying the almost totality of this organ and invading the venous system. The histological study of this splenic mass demonstrated to secondary splenic location of a grade 1 neuroendocrine tumor. As part of an investigation for a primary tumor, fibro scopy was performed and revealed an ulcerating-bourging fundic process with a histological study in favor of a grade 1 neuroendocrine tumor.

Typical presentation of pulmonary lepidic adenocarcinoma: a rare case report.

Bronchioloalveolar carcinoma (BAC) is a rare subtype of adenocarcinoma of lung with distinct features and distinctive characteristics. It accounts approximately for 4% of lung cancers. In the following study we report a rare observation of a 50 years old female with a clinical, radiological and histological presentation, which is typical of an invasive mucinous lepidic adenocarcinoma formerly named BAC.

Pancreatic solid serous cystadenoma treated by laparoscopy: Presentation of a new case report and review of the literature.

Solid serous cystadenoma is an uncommon benign pancreatic tumor, with only, including this case, 21 cases published so far. It is often misdiagnosis with other malignant pancreatic tumors. Below we report a new case of a solid serous cystadenoma of the pancreas treated by laparoscopic distal pancreatectomy in 53-year-old female who presented with epigastric pain. Histological and immunohistochemical examination revealed a solid serous cystadenoma of the pancreas. Preoperative diagnosis of this subtype of serous cystadenoma is difficult, and, due to its benign nature, conservative resection of the tumor is the recommended treatment. After analyzing the literature, including this case from our department, we discuss clinical presentation, imaging characteristics and histopathological findings, considering in particular difficulties in preoperative diagnosis, feasibility of laparoscopic resection.