Detalhe da pesquisa
1.
Cmah-dystrophin deficient mdx mice display an accelerated cardiac phenotype that is improved following peptide-PMO exon skipping treatment.
Hum Mol Genet
; 28(3): 396-406, 2019 02 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-30281092
2.
What is the level of dystrophin expression required for effective therapy of Duchenne muscular dystrophy?
J Muscle Res Cell Motil
; 40(2): 141-150, 2019 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-31289969
3.
How much dystrophin is enough: the physiological consequences of different levels of dystrophin in the mdx mouse.
Hum Mol Genet
; 24(15): 4225-37, 2015 Aug 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-25935000
4.
The transgenic expression of LARGE exacerbates the muscle phenotype of dystroglycanopathy mice.
Hum Mol Genet
; 23(7): 1842-55, 2014 Apr 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-24234655
5.
Muscle moment arms and sensitivity analysis of a mouse hindlimb musculoskeletal model.
J Anat
; 229(4): 514-35, 2016 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-27173448
6.
Preventing phosphorylation of dystroglycan ameliorates the dystrophic phenotype in mdx mouse.
Hum Mol Genet
; 21(20): 4508-20, 2012 Oct 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-22810924
7.
Ion channels as biomarkers of altered myogenesis in myofiber precursors of Duchenne muscular dystrophy.
Ann N Y Acad Sci
; 1534(1): 130-144, 2024 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-38517756
8.
Systemic AAV Gene Therapy Close to Clinical Trials for Several Neuromuscular Diseases.
Mol Ther
; 25(4): 834-835, 2017 04 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-28341564
9.
Longitudinal assessment of skeletal muscle functional mechanics in the DE50-MD dog model of Duchenne muscular dystrophy.
Dis Model Mech
; 16(12)2023 Dec 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-38050706
10.
Exon skipping and dystrophin restoration in patients with Duchenne muscular dystrophy after systemic phosphorodiamidate morpholino oligomer treatment: an open-label, phase 2, dose-escalation study.
Lancet
; 378(9791): 595-605, 2011 Aug 13.
Artigo
em Inglês
| MEDLINE | ID: mdl-21784508
11.
Designing translationally relevant preclinical studies of new therapeutics.
Exp Physiol
; 102(6): 616, 2017 06 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-28382753
12.
Physiological characterization of muscle strength with variable levels of dystrophin restoration in mdx mice following local antisense therapy.
Mol Ther
; 19(1): 165-71, 2011 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-20924363
13.
Chronic systemic therapy with low-dose morpholino oligomers ameliorates the pathology and normalizes locomotor behavior in mdx mice.
Mol Ther
; 19(2): 345-54, 2011 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-21102560
14.
Validation of DE50-MD dogs as a model for the brain phenotype of Duchenne muscular dystrophy.
Dis Model Mech
; 15(3)2022 03 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-35019137
15.
Serum inflammatory cytokines as disease biomarkers in the DE50-MD dog model of Duchenne muscular dystrophy.
Dis Model Mech
; 15(12)2022 12 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-36444978
16.
The skeletal muscle phenotype of the DE50-MD dog model of Duchenne muscular dystrophy.
Wellcome Open Res
; 7: 238, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-36865375
17.
Muscular dystrophies due to glycosylation defects: diagnosis and therapeutic strategies.
Curr Opin Neurol
; 24(5): 437-42, 2011 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-21825985
18.
Förster resonance energy transfer imaging in vivo with approximated radiative transfer equation.
Appl Opt
; 50(36): 6583-90, 2011 Dec 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-22193187
19.
Identification of qPCR reference genes suitable for normalising gene expression in the developing mouse embryo.
Wellcome Open Res
; 6: 197, 2021.
Artigo
em Inglês
| MEDLINE | ID: mdl-35509373
20.
The Pen Is Milder Than the Blade: Identification Marking Mice Using Ink on the Tail Appears More Humane Than Ear-Punching Even with Local Anaesthetic.
Animals (Basel)
; 11(6)2021 Jun 03.
Artigo
em Inglês
| MEDLINE | ID: mdl-34204900