Juvenile dermatomyositis forty years on: Case report.
Neuromuscul Disord
; 28(9): 791-797, 2018 09.
Article
em En
| MEDLINE
| ID: mdl-30064892
ABSTRACT
We present a case report of a 42 year old female, diagnosed at the age of 3 with Juvenile Dermatomyositis. The clinical course was severe and refractory to immunosuppressive therapy. Currently, she is mostly affected by severe muscle atrophy, large joint contractures, calcinosis, and a lipodystrophy associated metabolic syndrome with hypertriglyceridemia, insulin resistance, high total testosterone and hepatic steatosis. She developed Hodgkin´s lymphoma in the course of her disease. Personalized therapeutic choices are discussed as regards juvenile dermatomyositis complications.
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Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Limite:
Adult
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Child, preschool
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Female
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Humans
Idioma:
En
Ano de publicação:
2018
Tipo de documento:
Article