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Calcium bilirubinate sludge causes early onset of congenital biliary dilatation: a report of two cases.
Kato, Shoko; Kaneko, Kenitiro; Matsushita, Nozomi; Kurahashi, Shintaro; Osawa, Takaaki; Matsumura, Tatsuki; Saito, Takuya; Fukami, Yasuyuki; Komatsu, Shunichiro; Sano, Tsuyoshi.
Afiliação
  • Kato S; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Kaneko K; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan. kkaneko@aichi-med-u.ac.jp.
  • Matsushita N; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Kurahashi S; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Osawa T; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Matsumura T; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Saito T; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Fukami Y; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Komatsu S; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
  • Sano T; Department of Surgery, Aichi Medical University, 1-1 Yazakokarimata, Ngakute, Aichi, 480-1195, Japan.
Surg Case Rep ; 7(1): 92, 2021 Apr 13.
Article em En | MEDLINE | ID: mdl-33851282
BACKGROUND: Symptomatic congenital biliary dilatation (CBD) during early infancy is always characterized by cystic dilation of the common bile duct with a narrow segment connecting the pancreatic duct. CASE PRESENTATION: In two consecutive infants with a prenatal diagnosis of CBD, we found that biliary sludge had formed in the cyst upon the appearance of symptoms including acholic stool and hypertransaminasemia. Infrared absorption spectrometry revealed that the sludge consisted of calcium bilirubinate. CONCLUSION: We suggest that overproduction of bilirubin by neonatal hemolysis causes sedimentation of bilirubin calcium, resulting in obstruction of the narrow segment and development of symptoms.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Etiology_studies Idioma: En Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Etiology_studies Idioma: En Ano de publicação: 2021 Tipo de documento: Article