RESUMO
Anomalous systemic venous connection to left atrium is rare anomaly. Previously published cases described this anatomy in patients with left isomerism. Depending on the size of the atrial septal defect, patients usually present with varying degrees of cyanosis and right heart hypoplasia. Here, we report a case of anomalous systemic venous connection to left atrium in a newborn with the usual atrial arrangement.
Assuntos
Fibrilação Atrial , Comunicação Interatrial , Síndrome de Heterotaxia , Veias Pulmonares , Malformações Vasculares , Recém-Nascido , Humanos , Veias Pulmonares/anormalidades , Átrios do Coração/diagnóstico por imagem , Átrios do Coração/anormalidades , Comunicação Interatrial/complicações , Comunicação Interatrial/diagnósticoRESUMO
We describe an unusual example of double-outlet right atrium with separate atrioventricular junctions. The straddling and overriding tricuspid valve had two orifices, and the mitral valve was morphologically normal. An appropriate understanding of the morphology of the atrioventricular junctions, the valves, and the subvalvar apparatus, along with the location of the atrioventricular conduction axis, allowed for successful biventricular repair.