Detalhe da pesquisa
1.
Disturbances in mitochondrial bioenergetics and control quality and unbalanced redox homeostasis in the liver of a mouse model of mucopolysaccharidosis type II.
Mol Cell Biochem
; 2024 Mar 18.
Artigo
Inglês
| MEDLINE | ID: mdl-38498105
2.
N-Acetylglutamate and N-acetylmethionine compromise mitochondrial bioenergetics homeostasis and glutamate oxidation in brain of developing rats: Potential implications for the pathogenesis of ACY1 deficiency.
Biochem Biophys Res Commun
; 684: 149123, 2023 12 03.
Artigo
Inglês
| MEDLINE | ID: mdl-37871522
3.
Disruption of mitochondrial functions involving mitochondrial permeability transition pore opening caused by maleic acid in rat kidney.
J Bioenerg Biomembr
; 54(4): 203-213, 2022 Aug.
Artigo
Inglês
| MEDLINE | ID: mdl-35902433
4.
Ethylmalonic acid impairs bioenergetics by disturbing succinate and glutamate oxidation and induces mitochondrial permeability transition pore opening in rat cerebellum.
J Neurochem
; 158(2): 262-281, 2021 07.
Artigo
Inglês
| MEDLINE | ID: mdl-33837559
5.
Mechanism of a Flexible ICU Visiting Policy for Anxiety Symptoms Among Family Members in Brazil: A Path Mediation Analysis in a Cluster-Randomized Clinical Trial.
Crit Care Med
; 49(9): 1504-1512, 2021 09 01.
Artigo
Inglês
| MEDLINE | ID: mdl-33870915
6.
S-adenosylmethionine induces mitochondrial dysfunction, permeability transition pore opening and redox imbalance in subcellular preparations of rat liver.
J Bioenerg Biomembr
; 53(5): 525-539, 2021 10.
Artigo
Inglês
| MEDLINE | ID: mdl-34347214
7.
Disruption of mitochondrial functions and oxidative stress contribute to neurologic dysfunction in organic acidurias.
Arch Biochem Biophys
; 696: 108646, 2020 12 15.
Artigo
Inglês
| MEDLINE | ID: mdl-33098870
8.
Experimental evidence that maleic acid markedly compromises glutamate oxidation through inhibition of glutamate dehydrogenase and α-ketoglutarate dehydrogenase activities in kidney of developing rats.
Mol Cell Biochem
; 458(1-2): 99-112, 2019 Aug.
Artigo
Inglês
| MEDLINE | ID: mdl-31032535
9.
Concentration of Serum Vascular Endothelial Growth Factor (VEGF-D) and Its Correlation with Functional and Clinical Parameters in Patients with Lymphangioleiomyomatosis from a Brazilian Reference Center.
Lung
; 197(2): 139-146, 2019 04.
Artigo
Inglês
| MEDLINE | ID: mdl-30623243
10.
High vulnerability of the heart and liver to 3-hydroxypalmitic acid-induced disruption of mitochondrial functions in intact cell systems.
J Cell Biochem
; 119(9): 7678-7686, 2018 09.
Artigo
Inglês
| MEDLINE | ID: mdl-29923625
11.
cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca(2+) homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency.
Biochim Biophys Acta
; 1857(9): 1363-1372, 2016 09.
Artigo
Inglês
| MEDLINE | ID: mdl-27240720
12.
Bioenergetics dysfunction, mitochondrial permeability transition pore opening and lipid peroxidation induced by hydrogen sulfide as relevant pathomechanisms underlying the neurological dysfunction characteristic of ethylmalonic encephalopathy.
Biochim Biophys Acta Mol Basis Dis
; 1863(9): 2192-2201, 2017 09.
Artigo
Inglês
| MEDLINE | ID: mdl-28624490
13.
Impairment of GABAergic system contributes to epileptogenesis in glutaric acidemia type I.
Epilepsia
; 58(10): 1771-1781, 2017 10.
Artigo
Inglês
| MEDLINE | ID: mdl-28762469
14.
Uncoupling, metabolic inhibition and induction of mitochondrial permeability transition in rat liver mitochondria caused by the major long-chain hydroxyl monocarboxylic fatty acids accumulating in LCHAD deficiency.
Biochim Biophys Acta
; 1847(6-7): 620-8, 2015.
Artigo
Inglês
| MEDLINE | ID: mdl-25868874
15.
Disturbance of energy and redox homeostasis and reduction of Na+,K+-ATPase activity provoked by in vivo intracerebral administration of ethylmalonic acid to young rats.
Biochim Biophys Acta
; 1852(5): 759-67, 2015 May.
Artigo
Inglês
| MEDLINE | ID: mdl-25583115
16.
2-Methylcitric acid impairs glutamate metabolism and induces permeability transition in brain mitochondria.
J Neurochem
; 137(1): 62-75, 2016 Apr.
Artigo
Inglês
| MEDLINE | ID: mdl-26800654
17.
Ornithine and Homocitrulline Impair Mitochondrial Function, Decrease Antioxidant Defenses and Induce Cell Death in Menadione-Stressed Rat Cortical Astrocytes: Potential Mechanisms of Neurological Dysfunction in HHH Syndrome.
Neurochem Res
; 41(9): 2190-8, 2016 Sep.
Artigo
Inglês
| MEDLINE | ID: mdl-27161368
18.
Mitochondrial bioenergetics deregulation caused by long-chain 3-hydroxy fatty acids accumulating in LCHAD and MTP deficiencies in rat brain: a possible role of mPTP opening as a pathomechanism in these disorders?
Biochim Biophys Acta
; 1842(9): 1658-67, 2014 Sep.
Artigo
Inglês
| MEDLINE | ID: mdl-24946182
19.
Sulfite disrupts brain mitochondrial energy homeostasis and induces mitochondrial permeability transition pore opening via thiol group modification.
Biochim Biophys Acta
; 1842(9): 1413-22, 2014 Sep.
Artigo
Inglês
| MEDLINE | ID: mdl-24793416
20.
COVID-19 and lymphangioleiomyomatosis: Experience at a reference center and the potential impact of the use of mTOR inhibitors.
Am J Med Genet A
; 182(12): 3068-3070, 2020 12.
Artigo
Inglês
| MEDLINE | ID: mdl-32946196